Protein Substitutes in PKU; Their Historical Evolution

by Anne Daly, Sharon Evans, Alex Pinto, Catherine Ashmore, Anita MacDonald
Published 2021-02-01

An Observational Study Evaluating the Introduction of a Prolonged-Release Protein Substitute to the Dietary Management of Children with Phenylketonuria

by Anita MacDonald, Catherine Ashmore, Anne Daly, Alex Pinto, Sharon Evans
Published 2020-09-01

Casein Glycomacropeptide: An Alternative Protein Substitute in Tyrosinemia Type I

by Anne Daly, Sharon Evans, Alex Pinto, Catherine Ashmore, Anita MacDonald
Published 2021-09-01

A 3 Year Longitudinal Prospective Review Examining the Dietary Profile and Contribution Made by Special Low Protein Foods to Energy and Macronutrient Intake in Children with Phenyl...

by Anne Daly, Sharon Evans, Alex Pinto, Catherine Ashmore, Júlio César Rocha, Anita MacDonald
Published 2020-10-01

The Impact of the Use of Glycomacropeptide on Satiety and Dietary Intake in Phenylketonuria

by Anne Daly, Sharon Evans, Alex Pinto, Richard Jackson, Catherine Ashmore, Júlio César Rocha, Anita MacDonald
Published 2020-09-01

Preliminary Investigation to Review If a Glycomacropeptide Compared to L-Amino Acid Protein Substitute Alters the Pre- and Postprandial Amino Acid Profile in Children with Phenylke...

by Anne Daly, Sharon Evans, Alex Pinto, Richard Jackson, Catherine Ashmore, Júlio César Rocha, Anita MacDonald
Published 2020-08-01

The Use of Glycomacropeptide in Patients with Phenylketonuria: A Systematic Review and Meta-Analysis

by Maria João Pena, Alex Pinto, Anne Daly, Anita MacDonald, Luís Azevedo, Júlio César Rocha, Nuno Borges
Published 2018-11-01

Accidental Consumption of Aspartame in Phenylketonuria: Patient Experiences

by Ella Newbould, Alex Pinto, Sharon Evans, Suzanne Ford, Mike O’Driscoll, Catherine Ashmore, Anne Daly, Anita MacDonald
Published 2021-02-01

Protein Labelling Accuracy for UK Patients with PKU Following a Low Protein Diet

by Dilyana Kraleva, Sharon Evans, Alex Pinto, Anne Daly, Catherine Ashmore, Kiri Pointon-Bell, Júlio César Rocha, Anita MacDonald
Published 2020-11-01

Physical Growth of Patients with Hereditary Tyrosinaemia Type I: A Single-Centre Retrospective Study

by Ozlem Yilmaz, Anne Daly, Alex Pinto, Catherine Ashmore, Sharon Evans, Girish Gupte, Richard Jackson, Nurcan Yabanci Ayhan, Anita MacDonald
Published 2021-08-01

Protein Substitute Requirements of Patients with Phenylketonuria on BH4 Treatment: A Systematic Review and Meta-Analysis

by Fatma Ilgaz, Cyril Marsaux, Alex Pinto, Rani Singh, Carmen Rohde, Erdem Karabulut, Hülya Gökmen-Özel, Mirjam Kuhn, Anita MacDonald
Published 2021-03-01

The Effect of Glycomacropeptide versus Amino Acids on Phenylalanine and Tyrosine Variability over 24 Hours in Children with PKU: A Randomized Controlled Trial

by Anne Daly, Sharon Evans, Satnam Chahal, Saikat Santra, Alex Pinto, Cerys Gingell, Júlio César Rocha, Francjan van Spronsen, Richard Jackson, Anita MacDonald
Published 2019-02-01

Long-Term Growth in Phenylketonuria: A Systematic Review and Meta-Analysis

by Fatma Ilgaz, Alex Pinto, Hülya Gökmen-Özel, Julio César Rocha, Esther van Dam, Kirsten Ahring, Amaya Bélanger-Quintana, Katharina Dokoupil, Erdem Karabulut, Anita MacDonald
Published 2019-09-01

Natural Protein Tolerance and Metabolic Control in Patients with Hereditary Tyrosinaemia Type 1

by Ozlem Yilmaz, Anne Daly, Alex Pinto, Catherine Ashmore, Sharon Evans, Girish Gupte, Saikat Santra, Mary Anne Preece, Patrick Mckiernan, Steve Kitchen, Nurcan Yabanci Ayhan, Anita MacDonald
Published 2020-04-01

Growth and Body Composition in PKU Children—A Three-Year Prospective Study Comparing the Effects of L-Amino Acid to Glycomacropeptide Protein Substitutes

by Anne Daly, Wolfgang Högler, Nicola Crabtree, Nick Shaw, Sharon Evans, Alex Pinto, Richard Jackson, Boyd J Strauss, Gisela Wilcox, Júlio C. Rocha, Catherine Ashmore, Anita MacDonald
Published 2021-04-01

Metabolic Control of Patients with Phenylketonuria in a Portuguese Metabolic Centre Comparing Three Different Recommendations

by Viviane Kanufre, Manuela Ferreira Almeida, Catarina Sousa Barbosa, Carla Carmona, Anabela Bandeira, Esmeralda Martins, Sara Rocha, Arlindo Guimas, Rosa Ribeiro, Anita MacDonald, Alex Pinto, Júlio César Rocha
Published 2021-09-01

Over Restriction of Dietary Protein Allowance: The Importance of Ongoing Reassessment of Natural Protein Tolerance in Phenylketonuria

by Alex Pinto, Manuela Ferreira Almeida, Anita MacDonald, Paula Cristina Ramos, Sara Rocha, Arlindo Guimas, Rosa Ribeiro, Esmeralda Martins, Anabela Bandeira, Richard Jackson, Francjan van Spronsen, Anne Payne, Júlio César Rocha
Published 2019-04-01

A Three-Year Longitudinal Study Comparing Bone Mass, Density, and Geometry Measured by DXA, pQCT, and Bone Turnover Markers in Children with PKU Taking L-Amino Acid or Glycomacrope...

by Anne Daly, Wolfgang Högler, Nicola Crabtree, Nick Shaw, Sharon Evans, Alex Pinto, Richard Jackson, Catherine Ashmore, Júlio C. Rocha, Boyd J. Strauss, Gisela Wilcox, William D. Fraser, Jonathan C. Y. Tang, Anita MacDonald
Published 2021-06-01

Continuous use of glycomacropeptide in the nutritional management of patients with phenylketonuria: a clinical perspective

by Maria João Pena, Alex Pinto, Manuela Ferreira de Almeida, Catarina de Sousa Barbosa, Paula Cristina Ramos, Sara Rocha, Arlindo Guimas, Rosa Ribeiro, Esmeralda Martins, Anabela Bandeira, Cláudia Camila Dias, Anita MacDonald, Nuno Borges, Júlio César Rocha
Published 2021-02-01

Dietary Management, Clinical Status and Outcome of Patients with Citrin Deficiency in the UK

by Alex Pinto, Catherine Ashmore, Spyros Batzios, Anne Daly, Charlotte Dawson, Marjorie Dixon, Sharon Evans, Diane Green, Joanna Gribben, Inderdip Hunjan, Elisabeth Jameson, Camille Newby, Germaine Pierre, Sanjay Rajwal, Louise Robertson, Si Santra, Mark Sharrard, Roshni Vara, Lucy White, Gisela Wilcox, Ozlem Yilmaz, Anita MacDonald
Published 2020-10-01