Pulmonary hypertension secondary to pulmonary fibrosis: clinical data, histopathology and molecular insights

Abstract Pulmonary hypertension (PH) developing secondarily in pulmonary fibrosis (PF) patients (PF-PH) is a frequent co-morbidity. The high prevalence of PH in PF patients is very concerning since the presence of PH is a strong predictor of mortality in PF patients. Until recently, PH was thought t...

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Bibliographic Details
Main Authors: Grégoire Ruffenach, Jason Hong, Mylène Vaillancourt, Lejla Medzikovic, Mansoureh Eghbali
Format: Article
Language:English
Published: BMC 2020-11-01
Series:Respiratory Research
Subjects:
Online Access:http://link.springer.com/article/10.1186/s12931-020-01570-2