Genetic Cholestasis: Lessons from the Molecular Physiology of Bile Formation
Progressive familial intrahepatic cholestasis (PFIC) is a group of severe genetic cholestatic liver diseases of early life. PFIC types 1 and 2 are characterized by cholestasis and a low to normal serum gamma-glutamyltransferase (GGT) activity, whereas in PFIC type 3, the serum GGT activity is elevat...
Main Authors: | , |
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Format: | Article |
Language: | English |
Published: |
Hindawi Limited
2000-01-01
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Series: | Canadian Journal of Gastroenterology |
Online Access: | http://dx.doi.org/10.1155/2000/514172 |