Vitreoretinal Surgery and Panretinal Photocoagulation in a Patient with Multiple Large Retinal Capillary Hemangiomas (von Hippel-Lindau Disease): A Novel Approach

The authors present a novel surgical approach for the treatment of retinal capillary hemangiomas (RCHs) secondary to von Hippel-Lindau (VHL) disease. This is a case report of a 23-year-old male patient with VHL that presented with multiple large RCHs and a thick epiretinal membrane (ERM) in his left...

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Main Authors: Guilherme Sturzeneker, André Maia, Melina Morales, Rubens N. Belfort
Format: Article
Language:English
Published: Karger Publishers 2019-10-01
Series:Case Reports in Ophthalmology
Subjects:
Online Access:https://www.karger.com/Article/FullText/502970
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spelling doaj-2d72b120a8dd400ca5a48c876390ae9e2020-11-25T01:06:50ZengKarger PublishersCase Reports in Ophthalmology1663-26992019-10-0110332733310.1159/000502970502970Vitreoretinal Surgery and Panretinal Photocoagulation in a Patient with Multiple Large Retinal Capillary Hemangiomas (von Hippel-Lindau Disease): A Novel ApproachGuilherme SturzenekerAndré MaiaMelina MoralesRubens N. BelfortThe authors present a novel surgical approach for the treatment of retinal capillary hemangiomas (RCHs) secondary to von Hippel-Lindau (VHL) disease. This is a case report of a 23-year-old male patient with VHL that presented with multiple large RCHs and a thick epiretinal membrane (ERM) in his left eye, with best-corrected visual acuity (BCVA) of 20/80. This condition was surgically addressed with 23-gauge pars plana vitrectomy, ERM and internal limiting membrane peeling, and panretinal photocoagulation. Three monthly intravitreal injections of bevacizumab were administered after surgery. In a 14-month follow-up period, hemangiomas have regressed after laser therapy, macular anatomy has improved, retina remained completely attached, and there has been no development of new tumors or proliferative vitreoretinopathy. The patient achieved a BCVA of 20/40 in the treated eye. Panretinal photocoagulation combined with pars plana vitrectomy may be useful to reduce development of new capillary hemangiomas and reduce overall occurrence of complications in patients with VHL disease. Postoperative intravitreal injections of bevacizumab may have a role in this positive outcome.https://www.karger.com/Article/FullText/502970Retinal capillary hemangiomaVon Hippel-Lindau diseaseLaser photocoagulationVitreoretinal surgery
collection DOAJ
language English
format Article
sources DOAJ
author Guilherme Sturzeneker
André Maia
Melina Morales
Rubens N. Belfort
spellingShingle Guilherme Sturzeneker
André Maia
Melina Morales
Rubens N. Belfort
Vitreoretinal Surgery and Panretinal Photocoagulation in a Patient with Multiple Large Retinal Capillary Hemangiomas (von Hippel-Lindau Disease): A Novel Approach
Case Reports in Ophthalmology
Retinal capillary hemangioma
Von Hippel-Lindau disease
Laser photocoagulation
Vitreoretinal surgery
author_facet Guilherme Sturzeneker
André Maia
Melina Morales
Rubens N. Belfort
author_sort Guilherme Sturzeneker
title Vitreoretinal Surgery and Panretinal Photocoagulation in a Patient with Multiple Large Retinal Capillary Hemangiomas (von Hippel-Lindau Disease): A Novel Approach
title_short Vitreoretinal Surgery and Panretinal Photocoagulation in a Patient with Multiple Large Retinal Capillary Hemangiomas (von Hippel-Lindau Disease): A Novel Approach
title_full Vitreoretinal Surgery and Panretinal Photocoagulation in a Patient with Multiple Large Retinal Capillary Hemangiomas (von Hippel-Lindau Disease): A Novel Approach
title_fullStr Vitreoretinal Surgery and Panretinal Photocoagulation in a Patient with Multiple Large Retinal Capillary Hemangiomas (von Hippel-Lindau Disease): A Novel Approach
title_full_unstemmed Vitreoretinal Surgery and Panretinal Photocoagulation in a Patient with Multiple Large Retinal Capillary Hemangiomas (von Hippel-Lindau Disease): A Novel Approach
title_sort vitreoretinal surgery and panretinal photocoagulation in a patient with multiple large retinal capillary hemangiomas (von hippel-lindau disease): a novel approach
publisher Karger Publishers
series Case Reports in Ophthalmology
issn 1663-2699
publishDate 2019-10-01
description The authors present a novel surgical approach for the treatment of retinal capillary hemangiomas (RCHs) secondary to von Hippel-Lindau (VHL) disease. This is a case report of a 23-year-old male patient with VHL that presented with multiple large RCHs and a thick epiretinal membrane (ERM) in his left eye, with best-corrected visual acuity (BCVA) of 20/80. This condition was surgically addressed with 23-gauge pars plana vitrectomy, ERM and internal limiting membrane peeling, and panretinal photocoagulation. Three monthly intravitreal injections of bevacizumab were administered after surgery. In a 14-month follow-up period, hemangiomas have regressed after laser therapy, macular anatomy has improved, retina remained completely attached, and there has been no development of new tumors or proliferative vitreoretinopathy. The patient achieved a BCVA of 20/40 in the treated eye. Panretinal photocoagulation combined with pars plana vitrectomy may be useful to reduce development of new capillary hemangiomas and reduce overall occurrence of complications in patients with VHL disease. Postoperative intravitreal injections of bevacizumab may have a role in this positive outcome.
topic Retinal capillary hemangioma
Von Hippel-Lindau disease
Laser photocoagulation
Vitreoretinal surgery
url https://www.karger.com/Article/FullText/502970
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