The amount of calcifications in pseudoxanthoma elasticum patients is underestimated in computed tomographic imaging; a post-mortem correlation of histological and computed tomographic findings in two cases

Abstract Objectives Pseudoxanthoma elasticum (PXE) is a rare genetic disorder, characterised by elastic fibre degeneration and calcifications in multiple organ systems. Computed tomography (CT) imaging is a potential method to monitor disease progression in PXE patients; however, this method has not...

Full description

Bibliographic Details
Main Authors: Annelotte Vos, Guido Kranenburg, Pim A. de Jong, Willem P. T. M. Mali, Wim Van Hecke, Ronald L. A. W. Bleys, Ivana Isgum, Aryan Vink, Wilko Spiering
Format: Article
Language:English
Published: SpringerOpen 2018-06-01
Series:Insights into Imaging
Subjects:
Online Access:http://link.springer.com/article/10.1007/s13244-018-0621-6