Papillon-Lefèvre Syndrome and Basal Cell Carcinoma: A Case Study
Papillon–Lefèvre syndrome (PLS) is a rare autosomal recessive disorder characterized by palmoplantar keratoderma and early-onset periodontitis. It was first described by Papillon and Lefèvre in 1924. PLS is caused by mutations in the cathepsin-C (CTSC) gene. The development of malignant skin neoplas...
Main Authors: | , , , |
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Format: | Article |
Language: | English |
Published: |
Karger Publishers
2019-06-01
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Series: | Case Reports in Oncology |
Subjects: | |
Online Access: | https://www.karger.com/Article/FullText/500502 |