Translation of the quality-of-life measure for adults with primary ciliary dyskinesia and its application in patients in Brazil
ABSTRACT Primary ciliary dyskinesia (PCD) is a genetic disorder that is typically inherited in an autosomal recessive manner. It is clinically characterized by recurrent respiratory infections. However, its repercussions for patient quality of life should not be overlooked. Studies have shown that P...
Main Authors: | , , , , , , |
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Format: | Article |
Language: | English |
Published: |
Sociedade Brasileira de Pneumologia e Tisiologia
2019-04-01
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Series: | Jornal Brasileiro de Pneumologia |
Subjects: | |
Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1806-37132019000300300&lng=en&tlng=en |