Translation of the quality-of-life measure for adults with primary ciliary dyskinesia and its application in patients in Brazil

ABSTRACT Primary ciliary dyskinesia (PCD) is a genetic disorder that is typically inherited in an autosomal recessive manner. It is clinically characterized by recurrent respiratory infections. However, its repercussions for patient quality of life should not be overlooked. Studies have shown that P...

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Bibliographic Details
Main Authors: Ana Paula Lima de Queiroz, Rodrigo Abensur Athanazio, Mary Anne Kowal Olm, Bruna Rubbo, Yuri Reis Casal, Jane Lucas, Laura Behan
Format: Article
Language:English
Published: Sociedade Brasileira de Pneumologia e Tisiologia 2019-04-01
Series:Jornal Brasileiro de Pneumologia
Subjects:
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1806-37132019000300300&lng=en&tlng=en