Sturge Weber Syndrome

Sturge weber syndrome is a rare sporadic condition of mesodermal phacomatosis, also called encephalotrigeminal angio­matosis (synonyms : fourth phacomatosis or mother spot), is a neurocutaneous disorder with angiomas that involve the leptomeninges (leptomeningeal angiomas) and the skin of the face...

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Main Authors: Kazi Nilufar Moly, S.M. Abu Ahsan, Md. Shafiqul lslam
Format: Article
Language:English
Published: Bangabandhu Sheikh Mujib Medical University 2016-07-01
Series:Bangabandhu Sheikh Mujib Medical University Journal
Subjects:
Online Access:https://www.banglajol.info/index.php/BSMMUJ/article/view/28924
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spelling doaj-5484a3dd792e49abb43dd1be976b579b2020-11-24T22:08:17ZengBangabandhu Sheikh Mujib Medical UniversityBangabandhu Sheikh Mujib Medical University Journal2074-29082224-77502016-07-018110.3329/bsmmuj.v8i1.2892418539Sturge Weber SyndromeKazi Nilufar Moly0S.M. Abu Ahsan1Md. Shafiqul lslam2Department of Ophthalmology, BSMMU250 Beded General Hospital, Dist ThakurgoanDepartment of Ophthalmology, BSMMU Sturge weber syndrome is a rare sporadic condition of mesodermal phacomatosis, also called encephalotrigeminal angio­matosis (synonyms : fourth phacomatosis or mother spot), is a neurocutaneous disorder with angiomas that involve the leptomeninges (leptomeningeal angiomas) and the skin of the face (purple colored flat cutaneous haemangiomas ), typically in the ophthalmic (V1) and maxillary (V2) distributions of the trigeminal nerve. The hallmark of sturge weber syndrome is a facial cutaneous venous dilation, also referred to as a nevus flammeus or port wine stain (PWS). Because of the rarity, we report here a one & half year old male child who presented with features of the Sturge Weber Syndrome on both side of face. https://www.banglajol.info/index.php/BSMMUJ/article/view/28924AngiomaNevus flammeusHemangiomaPhakomatosisSturge Weber Syndrome
collection DOAJ
language English
format Article
sources DOAJ
author Kazi Nilufar Moly
S.M. Abu Ahsan
Md. Shafiqul lslam
spellingShingle Kazi Nilufar Moly
S.M. Abu Ahsan
Md. Shafiqul lslam
Sturge Weber Syndrome
Bangabandhu Sheikh Mujib Medical University Journal
Angioma
Nevus flammeus
Hemangioma
Phakomatosis
Sturge Weber Syndrome
author_facet Kazi Nilufar Moly
S.M. Abu Ahsan
Md. Shafiqul lslam
author_sort Kazi Nilufar Moly
title Sturge Weber Syndrome
title_short Sturge Weber Syndrome
title_full Sturge Weber Syndrome
title_fullStr Sturge Weber Syndrome
title_full_unstemmed Sturge Weber Syndrome
title_sort sturge weber syndrome
publisher Bangabandhu Sheikh Mujib Medical University
series Bangabandhu Sheikh Mujib Medical University Journal
issn 2074-2908
2224-7750
publishDate 2016-07-01
description Sturge weber syndrome is a rare sporadic condition of mesodermal phacomatosis, also called encephalotrigeminal angio­matosis (synonyms : fourth phacomatosis or mother spot), is a neurocutaneous disorder with angiomas that involve the leptomeninges (leptomeningeal angiomas) and the skin of the face (purple colored flat cutaneous haemangiomas ), typically in the ophthalmic (V1) and maxillary (V2) distributions of the trigeminal nerve. The hallmark of sturge weber syndrome is a facial cutaneous venous dilation, also referred to as a nevus flammeus or port wine stain (PWS). Because of the rarity, we report here a one & half year old male child who presented with features of the Sturge Weber Syndrome on both side of face.
topic Angioma
Nevus flammeus
Hemangioma
Phakomatosis
Sturge Weber Syndrome
url https://www.banglajol.info/index.php/BSMMUJ/article/view/28924
work_keys_str_mv AT kazinilufarmoly sturgewebersyndrome
AT smabuahsan sturgewebersyndrome
AT mdshafiqullslam sturgewebersyndrome
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