First case of childhood Takayasu arteritis from Syria: a case report

Abstract Background Takayasu arteritis is a systemic granulomatous inflammation affecting the large- and medium-sized vessels such as aorta, its main branches, and pulmonary and renal arteries. Childhood Takayasu arteritis is a subtype of Takayasu arteritis that affects the age group ranging from yo...

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Main Authors: Wafa Alwattar, Rawan Al khudari, Judy Naameh, Jia Batha, Raghad Almajzoub, Basheer Khalil
Format: Article
Language:English
Published: BMC 2021-09-01
Series:Journal of Medical Case Reports
Subjects:
Online Access:https://doi.org/10.1186/s13256-021-03077-w
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spelling doaj-5ab9375cb8f34a5492e6a3412fb573202021-09-26T11:49:13ZengBMCJournal of Medical Case Reports1752-19472021-09-011511810.1186/s13256-021-03077-wFirst case of childhood Takayasu arteritis from Syria: a case reportWafa Alwattar0Rawan Al khudari1Judy Naameh2Jia Batha3Raghad Almajzoub4Basheer Khalil5Department of Gynaecology and Obstetrics, Faculty of Medicine, Damascus UniversityDepartment of Paediatrics, Children’s University Hospital, Faculty of Medicine, Damascus UniversityDepartment of Gynaecology and Obstetrics, Faculty of Medicine, Damascus UniversityDepartment of Internal Medicine, Faculty of Medicine, Damascus UniversityDepartment of Gastrology, Faculty of Medicine, Damascus UniversityDivision of Rheumatology, Department of Paediatrics, Children’s University Hospital, Faculty of Medicine, Damascus UniversityAbstract Background Takayasu arteritis is a systemic granulomatous inflammation affecting the large- and medium-sized vessels such as aorta, its main branches, and pulmonary and renal arteries. Childhood Takayasu arteritis is a subtype of Takayasu arteritis that affects the age group ranging from young infants to late adolescents. Case presentation We report the first childhood Takayasu arteritis case from Syria, a 12-year-old Syrian girl presenting with nonspecific symptoms and signs plus ischemic clinical features in her left arm. She relapsed twice with different additional symptoms each time. Conclusions There is scarcity of reviews and studies on childhood Takayasu arteritis in Arabs. We aim to share our experience to keep childhood Takayasu arteritis in mind as a differential diagnosis in any child presenting with hypertension, absent or reduced peripheral arterial pulse, or blood pressure differences between extremities.https://doi.org/10.1186/s13256-021-03077-wTakayasu arteritisChildhoodPulselessnessArabsSyria
collection DOAJ
language English
format Article
sources DOAJ
author Wafa Alwattar
Rawan Al khudari
Judy Naameh
Jia Batha
Raghad Almajzoub
Basheer Khalil
spellingShingle Wafa Alwattar
Rawan Al khudari
Judy Naameh
Jia Batha
Raghad Almajzoub
Basheer Khalil
First case of childhood Takayasu arteritis from Syria: a case report
Journal of Medical Case Reports
Takayasu arteritis
Childhood
Pulselessness
Arabs
Syria
author_facet Wafa Alwattar
Rawan Al khudari
Judy Naameh
Jia Batha
Raghad Almajzoub
Basheer Khalil
author_sort Wafa Alwattar
title First case of childhood Takayasu arteritis from Syria: a case report
title_short First case of childhood Takayasu arteritis from Syria: a case report
title_full First case of childhood Takayasu arteritis from Syria: a case report
title_fullStr First case of childhood Takayasu arteritis from Syria: a case report
title_full_unstemmed First case of childhood Takayasu arteritis from Syria: a case report
title_sort first case of childhood takayasu arteritis from syria: a case report
publisher BMC
series Journal of Medical Case Reports
issn 1752-1947
publishDate 2021-09-01
description Abstract Background Takayasu arteritis is a systemic granulomatous inflammation affecting the large- and medium-sized vessels such as aorta, its main branches, and pulmonary and renal arteries. Childhood Takayasu arteritis is a subtype of Takayasu arteritis that affects the age group ranging from young infants to late adolescents. Case presentation We report the first childhood Takayasu arteritis case from Syria, a 12-year-old Syrian girl presenting with nonspecific symptoms and signs plus ischemic clinical features in her left arm. She relapsed twice with different additional symptoms each time. Conclusions There is scarcity of reviews and studies on childhood Takayasu arteritis in Arabs. We aim to share our experience to keep childhood Takayasu arteritis in mind as a differential diagnosis in any child presenting with hypertension, absent or reduced peripheral arterial pulse, or blood pressure differences between extremities.
topic Takayasu arteritis
Childhood
Pulselessness
Arabs
Syria
url https://doi.org/10.1186/s13256-021-03077-w
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