UP-TO-DATE MANAGEMENT OF LIVER DISEASE AND COMPLICATIONS IN CYSTIC FIBROSIS AND TRANSITION OF ADOLESCENTS FROM PEDIATRIC TO ADULT CARE

• Main Authors: Marina Praprotnik, Nevenka Bratanič, Jernej Brecelj, Matjaž Fležar, Uroš Krivec
• Format: Article
• Language: English
• Published: Slovenian Medical Association 2015-05-01
• Series: Zdravniški Vestnik
• Subjects: diabetes mellitus; osteopenia; nutrition; cirrhosis; transition
• Online Access: http://vestnik.szd.si/index.php/ZdravVest/article/view/1228

<p>Cystic fibrosis (CF) is the most common autosomal recessive lethal hereditary disorder among whites. Survival of patients with CF has progressively improved over the last four decades.</p><p>As life expectancy has been greatly extended, complications like osteopenia and CF-related diabetes mellitus (CFRDM) occur. In our article, a new management of these two complications is described.</p><p>Gastrointestinal tract, exocrine pancreas and liver are also affected in CF.</p><p>Maintaining good nutrition while treating pancreatic insufficiency, treating gastroesophageal reflux disease and treating liver disease are very important issues in the treatment gastrointestinal tract disease in CF.</p><p>As the CF patient population median survival increases,  a growing number of adolescents require care in the adult health care system which must be capable of responding appropriately to their needs.</p><p>We present a model of transition from paediatric to adult medical care in our CF center.</p>