Presentation, diagnosis and clinical course of the spectrum of progressive-fibrosing interstitial lung diseases
Although these conditions are rare, a proportion of patients with interstitial lung diseases (ILDs) may develop a progressive-fibrosing phenotype. Progressive fibrosis is associated with worsening respiratory symptoms, lung function decline, limited response to immunomodulatory therapies, decreased...
Main Authors: | , , , , , , , , , , |
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Format: | Article |
Language: | English |
Published: |
European Respiratory Society
2018-12-01
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Series: | European Respiratory Review |
Online Access: | http://err.ersjournals.com/content/27/150/180076.full |