Presentation, diagnosis and clinical course of the spectrum of progressive-fibrosing interstitial lung diseases

Although these conditions are rare, a proportion of patients with interstitial lung diseases (ILDs) may develop a progressive-fibrosing phenotype. Progressive fibrosis is associated with worsening respiratory symptoms, lung function decline, limited response to immunomodulatory therapies, decreased...

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Bibliographic Details
Main Authors: Vincent Cottin, Nikhil A. Hirani, David L. Hotchkin, Anoop M. Nambiar, Takashi Ogura, María Otaola, Dirk Skowasch, Jong Sun Park, Hataya K. Poonyagariyagorn, Wim Wuyts, Athol U. Wells
Format: Article
Language:English
Published: European Respiratory Society 2018-12-01
Series:European Respiratory Review
Online Access:http://err.ersjournals.com/content/27/150/180076.full