Oral lesions in tuberous sclerosis
Tuberous sclerosis complex (TSC) is an autosomal-dominant neurocutaneous syndrome with an approximate incidence of 1 in 10,000–50,000. The cardinal features of TSC are skin lesions, convulsive seizures, and mental retardation. Here, we report a case of TSC in a male patient who presented with oral a...
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Wolters Kluwer Medknow Publications
2018-01-01
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doaj-995212d51e554269acbb6116efa0263a2020-11-24T20:49:01ZengWolters Kluwer Medknow PublicationsJournal of Indian Academy of Oral Medicine and Radiology0972-13632018-01-0130218919210.4103/jiaomr.jiaomr_24_18Oral lesions in tuberous sclerosisLakshmi S ReddyTulika SinghVinod K ReddySachin MittalTuberous sclerosis complex (TSC) is an autosomal-dominant neurocutaneous syndrome with an approximate incidence of 1 in 10,000–50,000. The cardinal features of TSC are skin lesions, convulsive seizures, and mental retardation. Here, we report a case of TSC in a male patient who presented with oral and cutaneous manifestations without mental retardation or history of convulsive seizures, which is very rarely reported to the best of authors' knowledge.http://www.jiaomr.in/article.asp?issn=0972-1363;year=2018;volume=30;issue=2;spage=189;epage=192;aulast=ReddyAngiofibromaastrocytomahamartomas |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Lakshmi S Reddy Tulika Singh Vinod K Reddy Sachin Mittal |
spellingShingle |
Lakshmi S Reddy Tulika Singh Vinod K Reddy Sachin Mittal Oral lesions in tuberous sclerosis Journal of Indian Academy of Oral Medicine and Radiology Angiofibroma astrocytoma hamartomas |
author_facet |
Lakshmi S Reddy Tulika Singh Vinod K Reddy Sachin Mittal |
author_sort |
Lakshmi S Reddy |
title |
Oral lesions in tuberous sclerosis |
title_short |
Oral lesions in tuberous sclerosis |
title_full |
Oral lesions in tuberous sclerosis |
title_fullStr |
Oral lesions in tuberous sclerosis |
title_full_unstemmed |
Oral lesions in tuberous sclerosis |
title_sort |
oral lesions in tuberous sclerosis |
publisher |
Wolters Kluwer Medknow Publications |
series |
Journal of Indian Academy of Oral Medicine and Radiology |
issn |
0972-1363 |
publishDate |
2018-01-01 |
description |
Tuberous sclerosis complex (TSC) is an autosomal-dominant neurocutaneous syndrome with an approximate incidence of 1 in 10,000–50,000. The cardinal features of TSC are skin lesions, convulsive seizures, and mental retardation. Here, we report a case of TSC in a male patient who presented with oral and cutaneous manifestations without mental retardation or history of convulsive seizures, which is very rarely reported to the best of authors' knowledge. |
topic |
Angiofibroma astrocytoma hamartomas |
url |
http://www.jiaomr.in/article.asp?issn=0972-1363;year=2018;volume=30;issue=2;spage=189;epage=192;aulast=Reddy |
work_keys_str_mv |
AT lakshmisreddy orallesionsintuberoussclerosis AT tulikasingh orallesionsintuberoussclerosis AT vinodkreddy orallesionsintuberoussclerosis AT sachinmittal orallesionsintuberoussclerosis |
_version_ |
1716807089320361984 |