Over Restriction of Dietary Protein Allowance: The Importance of Ongoing Reassessment of Natural Protein Tolerance in Phenylketonuria
Phenylalanine (Phe) tolerance is highly variable in phenylketonuria (PKU) and rarely described in patients aged ≥12 years. Patients ≥12 years of age with PKU were systematically challenged with additional natural protein (NP) if blood Phe levels remained below 480 µmol/L (i.e., upper target blood Ph...
Main Authors: | Alex Pinto, Manuela Ferreira Almeida, Anita MacDonald, Paula Cristina Ramos, Sara Rocha, Arlindo Guimas, Rosa Ribeiro, Esmeralda Martins, Anabela Bandeira, Richard Jackson, Francjan van Spronsen, Anne Payne, Júlio César Rocha |
---|---|
Format: | Article |
Language: | English |
Published: |
MDPI AG
2019-04-01
|
Series: | Nutrients |
Subjects: | |
Online Access: | https://www.mdpi.com/2072-6643/11/5/995 |
Similar Items
-
Metabolic Control of Patients with Phenylketonuria in a Portuguese Metabolic Centre Comparing Three Different Recommendations
by: Viviane Kanufre, et al.
Published: (2021-09-01) -
Incidence of Phenylketonuria in Southern Iran
by: Asadollah Habib, et al.
Published: (2010-06-01) -
Difficulties in maintaining diet in patients with phenylketonuria
by: Kamila Morawska, et al.
Published: (2018-03-01) -
Phenylketonuria (PKU): A problem solved?
by: Christine S. Brown, et al.
Published: (2016-03-01) -
Prevention of maternal phenylketonuria. Dietary management in the preconception period and during pregnancy
by: Joanna Żółkowska, et al.
Published: (2018-03-01)