Pulmonary atresia with ventricular septal defect and major aorto-pulmonary collateral arteries in a young adult

Pulmonary atresia with ventricular septal defect (PA-VSD) and pulmonary blood supply arising from the aorta in the form of major aortopulmonary collateral circulation (MAPCAs) surviving in the adulthood is a rare occurrence. It is usually fatal in the infancy without surgical repair. We report the c...

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Bibliographic Details
Main Author: Rajshree U Dhadve
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2020-01-01
Series:Medical Journal of Dr. D.Y. Patil Vidyapeeth
Subjects:
Online Access:http://www.mjdrdypv.org/article.asp?issn=2589-8302;year=2020;volume=13;issue=4;spage=403;epage=405;aulast=Dhadve
Description
Summary:Pulmonary atresia with ventricular septal defect (PA-VSD) and pulmonary blood supply arising from the aorta in the form of major aortopulmonary collateral circulation (MAPCAs) surviving in the adulthood is a rare occurrence. It is usually fatal in the infancy without surgical repair. We report the case of a 25-year-old female with clinical and imaging findings of PA-VSD. She had previous episodes of cyanosis and exertional breathlessness which she could tolerate without much hampering of day-to-day activity. The current presentation was due to symptoms of bacterial infection which led to the diagnosis of the underlying complex cardiovascular malformation.
ISSN:2589-8302
2589-8310