Para aortic ganglioneuroma presenting as Cushing′s syndrome

Para aortic ganglioneuroma presenting as Cushing′s syndrome

We present a case of an eight-year-old female presenting with four months history of progressive weight gain, short stature, obesity, mild acanthosis, moon facies and buffalo hump. Biochemically, low-dose and high-dose Dexamethasone tests were not suppressible, ACTH was raised and 24h urinary metane...

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Bibliographic Details
Main Authors: S Jaya Ram Reddy, G Purushottam, K Pandurangarao, P T Ravi Chander
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2007-01-01
Series:Indian Journal of Urology
Subjects:
Cushing′s syndrome
ectopic ACTH
ganglioneuroma
para aortic
Online Access:http://www.indianjurol.com/article.asp?issn=0970-1591;year=2007;volume=23;issue=4;spage=471;epage=473;aulast=Reddy
Description
Summary:We present a case of an eight-year-old female presenting with four months history of progressive weight gain, short stature, obesity, mild acanthosis, moon facies and buffalo hump. Biochemically, low-dose and high-dose Dexamethasone tests were not suppressible, ACTH was raised and 24h urinary metanephrines were normal. The CECT scan showed a 3cm paraganglioma. Tumor was excised via 11 th rib transcostal approach and the mass was found arising from the sympathetic chain. Histopathology was suggestive of ganglioneuroma positive for ACTH immunostaining.
ISSN:0970-1591
1998-3824

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