Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y Reconstruction

Abstract A 1-year-old girl had pancreaticobiliary maljunction, a choledochal cyst, and polycystic kidney. At the age of 4 years, she was treated by resection of the choledochal cyst and Roux-en-Y reconstruction because of the cyst's risk of cancer. She was diagnosed as having congenital hepatic...

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Main Authors:	Tokio Sugiura, Takeshi Endo, Koichi Ito, Kenji Goto, Yoko Sato, Satoshi Kondo, Tatsuya Suzuki, Takashi Hashimoto
Format:	Article
Language:	English
Published:	Georg Thieme Verlag KG 2013-03-01
Series:	European Journal of Pediatric Surgery Reports
Subjects:	congenital hepatic fibrosis pancreaticobiliary maljunction cholangitis roux-en-y reconstruction liver transplantation
Online Access:	http://www.thieme-connect.de/DOI/DOI?10.1055/s-0033-1341420

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spelling	doaj-bfd6eb61434b47ca84caca472ec79b3a2020-11-25T03:16:22ZengGeorg Thieme Verlag KGEuropean Journal of Pediatric Surgery Reports2194-76192194-76272013-03-01010104304510.1055/s-0033-1341420Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y ReconstructionTokio Sugiura0Takeshi Endo1Koichi Ito2Kenji Goto3Yoko Sato4Satoshi Kondo5Tatsuya Suzuki6Takashi Hashimoto7Department of Pediatrics and Neonatology, Nagoya City University, Nagoya, JapanDepartment of Pediatrics and Neonatology, Nagoya City University, Nagoya, JapanDepartment of Pediatrics and Neonatology, Nagoya City University, Nagoya, JapanDepartment of Pediatrics and Neonatology, Nagoya City University, Nagoya, JapanDepartment of Pediatric Surgery, Nagoya City West Medical Center, Nagoya, JapanDepartment of Pediatric Surgery, Nagoya City University, Nagoya, JapanDepartment of Pediatric Surgery, Fujita Health University School of Medicine, Toyoake, JapanDepartment of Pediatric Surgery, Fujita Health University School of Medicine, Toyoake, JapanAbstract A 1-year-old girl had pancreaticobiliary maljunction, a choledochal cyst, and polycystic kidney. At the age of 4 years, she was treated by resection of the choledochal cyst and Roux-en-Y reconstruction because of the cyst's risk of cancer. She was diagnosed as having congenital hepatic fibrosis based on the histological findings. Postoperatively, she suffered recurrent fever of unknown origin, refractory to several antibiotics. At the age of 6 years, she underwent living donor liver transplantation from her father. Multi-drug-resistant Pseudomonas aeruginosa was cultured in the recipient's liver. After liver transplantation, she had no episodes of recurrent fever. Roux-en-Y reconstruction should be avoided for ductal plate malformations such as congenital hepatic fibrosis.http://www.thieme-connect.de/DOI/DOI?10.1055/s-0033-1341420congenital hepatic fibrosispancreaticobiliary maljunctioncholangitisroux-en-y reconstructionliver transplantation
collection	DOAJ
language	English
format	Article
sources	DOAJ
author	Tokio Sugiura Takeshi Endo Koichi Ito Kenji Goto Yoko Sato Satoshi Kondo Tatsuya Suzuki Takashi Hashimoto
spellingShingle	Tokio Sugiura Takeshi Endo Koichi Ito Kenji Goto Yoko Sato Satoshi Kondo Tatsuya Suzuki Takashi Hashimoto Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y Reconstruction European Journal of Pediatric Surgery Reports congenital hepatic fibrosis pancreaticobiliary maljunction cholangitis roux-en-y reconstruction liver transplantation
author_facet	Tokio Sugiura Takeshi Endo Koichi Ito Kenji Goto Yoko Sato Satoshi Kondo Tatsuya Suzuki Takashi Hashimoto
author_sort	Tokio Sugiura
title	Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y Reconstruction
title_short	Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y Reconstruction
title_full	Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y Reconstruction
title_fullStr	Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y Reconstruction
title_full_unstemmed	Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y Reconstruction
title_sort	recurrent cholangitis with congenital hepatic fibrosis and pancreaticobiliary maljunction after roux-en-y reconstruction
publisher	Georg Thieme Verlag KG
series	European Journal of Pediatric Surgery Reports
issn	2194-7619 2194-7627
publishDate	2013-03-01
description	Abstract A 1-year-old girl had pancreaticobiliary maljunction, a choledochal cyst, and polycystic kidney. At the age of 4 years, she was treated by resection of the choledochal cyst and Roux-en-Y reconstruction because of the cyst's risk of cancer. She was diagnosed as having congenital hepatic fibrosis based on the histological findings. Postoperatively, she suffered recurrent fever of unknown origin, refractory to several antibiotics. At the age of 6 years, she underwent living donor liver transplantation from her father. Multi-drug-resistant Pseudomonas aeruginosa was cultured in the recipient's liver. After liver transplantation, she had no episodes of recurrent fever. Roux-en-Y reconstruction should be avoided for ductal plate malformations such as congenital hepatic fibrosis.
topic	congenital hepatic fibrosis pancreaticobiliary maljunction cholangitis roux-en-y reconstruction liver transplantation
url	http://www.thieme-connect.de/DOI/DOI?10.1055/s-0033-1341420
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Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y Reconstruction

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