Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y Reconstruction
Abstract A 1-year-old girl had pancreaticobiliary maljunction, a choledochal cyst, and polycystic kidney. At the age of 4 years, she was treated by resection of the choledochal cyst and Roux-en-Y reconstruction because of the cyst's risk of cancer. She was diagnosed as having congenital hepatic...
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Georg Thieme Verlag KG
2013-03-01
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doaj-bfd6eb61434b47ca84caca472ec79b3a2020-11-25T03:16:22ZengGeorg Thieme Verlag KGEuropean Journal of Pediatric Surgery Reports2194-76192194-76272013-03-01010104304510.1055/s-0033-1341420Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y ReconstructionTokio Sugiura0Takeshi Endo1Koichi Ito2Kenji Goto3Yoko Sato4Satoshi Kondo5Tatsuya Suzuki6Takashi Hashimoto7Department of Pediatrics and Neonatology, Nagoya City University, Nagoya, JapanDepartment of Pediatrics and Neonatology, Nagoya City University, Nagoya, JapanDepartment of Pediatrics and Neonatology, Nagoya City University, Nagoya, JapanDepartment of Pediatrics and Neonatology, Nagoya City University, Nagoya, JapanDepartment of Pediatric Surgery, Nagoya City West Medical Center, Nagoya, JapanDepartment of Pediatric Surgery, Nagoya City University, Nagoya, JapanDepartment of Pediatric Surgery, Fujita Health University School of Medicine, Toyoake, JapanDepartment of Pediatric Surgery, Fujita Health University School of Medicine, Toyoake, JapanAbstract A 1-year-old girl had pancreaticobiliary maljunction, a choledochal cyst, and polycystic kidney. At the age of 4 years, she was treated by resection of the choledochal cyst and Roux-en-Y reconstruction because of the cyst's risk of cancer. She was diagnosed as having congenital hepatic fibrosis based on the histological findings. Postoperatively, she suffered recurrent fever of unknown origin, refractory to several antibiotics. At the age of 6 years, she underwent living donor liver transplantation from her father. Multi-drug-resistant Pseudomonas aeruginosa was cultured in the recipient's liver. After liver transplantation, she had no episodes of recurrent fever. Roux-en-Y reconstruction should be avoided for ductal plate malformations such as congenital hepatic fibrosis.http://www.thieme-connect.de/DOI/DOI?10.1055/s-0033-1341420congenital hepatic fibrosispancreaticobiliary maljunctioncholangitisroux-en-y reconstructionliver transplantation |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Tokio Sugiura Takeshi Endo Koichi Ito Kenji Goto Yoko Sato Satoshi Kondo Tatsuya Suzuki Takashi Hashimoto |
spellingShingle |
Tokio Sugiura Takeshi Endo Koichi Ito Kenji Goto Yoko Sato Satoshi Kondo Tatsuya Suzuki Takashi Hashimoto Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y Reconstruction European Journal of Pediatric Surgery Reports congenital hepatic fibrosis pancreaticobiliary maljunction cholangitis roux-en-y reconstruction liver transplantation |
author_facet |
Tokio Sugiura Takeshi Endo Koichi Ito Kenji Goto Yoko Sato Satoshi Kondo Tatsuya Suzuki Takashi Hashimoto |
author_sort |
Tokio Sugiura |
title |
Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y Reconstruction |
title_short |
Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y Reconstruction |
title_full |
Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y Reconstruction |
title_fullStr |
Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y Reconstruction |
title_full_unstemmed |
Recurrent Cholangitis with Congenital Hepatic Fibrosis and Pancreaticobiliary Maljunction after Roux-en-Y Reconstruction |
title_sort |
recurrent cholangitis with congenital hepatic fibrosis and pancreaticobiliary maljunction after roux-en-y reconstruction |
publisher |
Georg Thieme Verlag KG |
series |
European Journal of Pediatric Surgery Reports |
issn |
2194-7619 2194-7627 |
publishDate |
2013-03-01 |
description |
Abstract
A 1-year-old girl had pancreaticobiliary maljunction, a choledochal cyst, and polycystic kidney. At the age of 4 years, she was treated by resection of the choledochal cyst and Roux-en-Y reconstruction because of the cyst's risk of cancer. She was diagnosed as having congenital hepatic fibrosis based on the histological findings. Postoperatively, she suffered recurrent fever of unknown origin, refractory to several antibiotics. At the age of 6 years, she underwent living donor liver transplantation from her father. Multi-drug-resistant Pseudomonas aeruginosa was cultured in the recipient's liver. After liver transplantation, she had no episodes of recurrent fever. Roux-en-Y reconstruction should be avoided for ductal plate malformations such as congenital hepatic fibrosis. |
topic |
congenital hepatic fibrosis pancreaticobiliary maljunction cholangitis roux-en-y reconstruction liver transplantation |
url |
http://www.thieme-connect.de/DOI/DOI?10.1055/s-0033-1341420 |
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