Primary Angiitis of the Central Nervous System

Primary Angiitis of the Central Nervous System

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Primary angiitis of the central nervous system (PACNS) is an idiopathic disorder (vasculitis) restricted to the central nervous system (CNS). It often presents with focal neurological deficits suggesting stroke or a combination of confusion and headache. We herein report three cases with various com...

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Bibliographic Details
Main Authors: Hossein Pourmahmoodian, Hossein Ali Ghelichnia Omrani, Mohammad Hossein Harrirchian, Mojdeh Ghabaee, Babak Zamani, Majid Ghaffarpour
Format: Article
Language:English
Published: Tehran University of Medical Sciences 2012-03-01
Series:Acta Medica Iranica
Subjects:
Vasculitis
Central nervous system
Angiography
Online Access:https://acta.tums.ac.ir/index.php/acta/article/view/3886
Description
Summary:Primary angiitis of the central nervous system (PACNS) is an idiopathic disorder (vasculitis) restricted to the central nervous system (CNS). It often presents with focal neurological deficits suggesting stroke or a combination of confusion and headache. We herein report three cases with various combinations of fever, partial seizure, encephalopathy, paresis, headache and ataxia. One of them was initially treated as herpes simplex meningoencephalitis, but further investigations revealed primary angiitis. Primary angiitis of the CNS has protean manifestations and should always be considered in patients suspicious to have CNS infection or stroke, particularly who does not respond to the routine treatments. Clinical data, exclusion of differential diagnoses and typical angiography seem to be enough to justify the diagnosis in the majority of cases.
ISSN:0044-6025
1735-9694

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