Chaotic activation of developmental signalling pathways drives idiopathic pulmonary fibrosis
Idiopathic pulmonary fibrosis (IPF) is characterised by an important remodelling of lung parenchyma. Current evidence indicates that the disease is triggered by alveolar epithelium activation following chronic lung injury, resulting in alveolar epithelial type 2 cell hyperplasia and bronchiolisation...
Main Authors: | , , , , , , |
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Format: | Article |
Language: | English |
Published: |
European Respiratory Society
2020-11-01
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Series: | European Respiratory Review |
Online Access: | http://err.ersjournals.com/content/29/158/190140.full |