Search Results - Jonathan D. Cooper

Refine Results
  1. 1

    Top-down and bottom-up propagation of disease in the neuronal ceroid lipofuscinoses by John R. Ostergaard, Hemanth R. Nelvagal, Hemanth R. Nelvagal, Jonathan D. Cooper, Jonathan D. Cooper, Jonathan D. Cooper

    Published in Frontiers in Neurology (2022-11-01)
    Get full text
    Article


  2. 2

    Enteric nervous system disease in neuronopathic lysosomal storage disorders by Ewa A. Ziółkowska, Robert O. Heuckeroth, Jonathan D. Cooper

    Published in Neural Regeneration Research (2026-08-01)
    Get full text
    Article


  3. 3

    Regional and cellular neuropathology in the palmitoyl protein thioesterase-1 null mutant mouse model of infantile neuronal ceroid lipofuscinosis by Ellen Bible, Praveena Gupta, Sandra L Hofmann, Jonathan D Cooper

    Published in Neurobiology of Disease (2004-07-01)
    Get full text
    Article


  4. 4

    Thalamocortical neuron loss and localized astrocytosis in the Cln3Δex7/8 knock-in mouse model of Batten disease by Charlie C. Pontikis, Susan L. Cotman, Marcy E. MacDonald, Jonathan D. Cooper

    Published in Neurobiology of Disease (2005-12-01)
    Get full text
    Article


  5. 5

    Neurodegeneration and Epilepsy in a Zebrafish Model of CLN3 Disease (Batten Disease). by Kim Wager, Anselm A Zdebik, Sonia Fu, Jonathan D Cooper, Robert J Harvey, Claire Russell

    Published in PLoS ONE (2016-01-01)
    Get full text
    Article


  6. 6

    Cellular trafficking and fate mapping of cells within the nervous system after in utero hematopoietic cell transplantation by Matthew T. Grant, Hemanth Ramesh Nelvagal, Maria Tecos, Amal Hamed, Kerry Swanson, Jonathan D. Cooper, Jesse D. Vrecenak

    Published in Communications Biology (2024-12-01)
    Get full text
    Article


  7. 7

    Correction: Disruption of the Autophagy-Lysosome Pathway Is Involved in Neuropathology of the Mouse Model of Neuronal Ceroid Lipofuscinosis. by Melanie Thelen, Markus Damme, Michaela Schweizer, Christian Hagel, Andrew M.S. Wong, Jonathan D. Cooper, Thomas Braulke, Giovanna Galliciotti

    Published in PLoS ONE (2012-01-01)
    Get full text
    Article


  8. 8

    Disruption of the autophagy-lysosome pathway is involved in neuropathology of the nclf mouse model of neuronal ceroid lipofuscinosis. by Melanie Thelen, Markus Damme, Michaela Schweizer, Christian Hagel, Andrew M S Wong, Jonathan D Cooper, Thomas Braulke, Giovanna Galliciotti

    Published in PLoS ONE (2012-01-01)
    Get full text
    Article


  9. 9

    Compromised astrocyte function and survival negatively impact neurons in infantile neuronal ceroid lipofuscinosis by Jenny Lange, Luke J. Haslett, Emyr Lloyd-Evans, Jennifer M. Pocock, Mark S. Sands, Brenda P. Williams, Jonathan D. Cooper

    Published in Acta Neuropathologica Communications (2018-08-01)
    Get full text
    Article


  10. 10

    Genetically Corrected iPSC-Derived Neural Stem Cell Grafts Deliver Enzyme Replacement to Affect CNS Disease in Sanfilippo B Mice by Don Clarke, Yewande Pearse, Shih-hsin Kan, Steven Q. Le, Valentina Sanghez, Jonathan D. Cooper, Patricia I. Dickson, Michelina Iacovino

    Get full text
    Article


  11. 11

    Progressive thalamocortical neuron loss in Cln5 deficient mice: Distinct effects in Finnish variant late infantile NCL by Carina von Schantz, Catherine Kielar, Stine N. Hansen, Charlie C. Pontikis, Noreen A. Alexander, Outi Kopra, Anu Jalanko, Jonathan D. Cooper

    Published in Neurobiology of Disease (2009-05-01)
    Get full text
    Article


  12. 12

    Successive neuron loss in the thalamus and cortex in a mouse model of infantile neuronal ceroid lipofuscinosis by Catherine Kielar, Lucy Maddox, Ellen Bible, Charlie C. Pontikis, Shannon L. Macauley, Megan A. Griffey, Michael Wong, Mark S. Sands, Jonathan D. Cooper

    Published in Neurobiology of Disease (2007-01-01)
    Get full text
    Article


  13. 13

    Visual deficits in a mouse model of Batten disease are the result of optic nerve degeneration and loss of dorsal lateral geniculate thalamic neurons by Jill M. Weimer, Andrew W. Custer, Jared W. Benedict, Noreen A. Alexander, Evan Kingsley, Howard J. Federoff, Jonathan D. Cooper, David A. Pearce

    Published in Neurobiology of Disease (2006-05-01)
    Get full text
    Article


  14. 14

    IgG entry and deposition are components of the neuroimmune response in Batten disease by Ming J. Lim, Noreen Alexander, Jared W. Benedict, Subrata Chattopadhyay, Stephen J.A. Shemilt, Christopher J. Guérin, Jonathan D. Cooper, David A. Pearce

    Published in Neurobiology of Disease (2007-02-01)
    Get full text
    Article


  15. 15

    Antibiotic treatment reveals the contributions of the gut microbiome to CLN2 disease in the central and enteric nervous system by Ewa A. Ziółkowska, Paris Nix, Bartłomiej Olszowy, Letitia L. Williams, Elizabeth M. Eultgen, Agnieszka Nowacka, Marta Celorrio, Stuart H Friess, Robert O. Heuckeroth, Jonathan D. Cooper

    Published in Scientific Reports (2026-04-01)
    Get full text
    Article


  16. 16

    Gene therapy ameliorates spontaneous seizures associated with cortical neuron loss in a Cln2R207X mouse model by Keigo Takahashi, Elizabeth M. Eultgen, Sophie H. Wang, Nicholas R. Rensing, Hemanth R. Nelvagal, Joshua T. Dearborn, Olivier Danos, Nicholas Buss, Mark S. Sands, Michael Wong, Jonathan D. Cooper

    Published in The Journal of Clinical Investigation (2023-06-01)
    Get full text
    Article


  17. 17

    Brain transplantation of genetically corrected Sanfilippo type B neural stem cells induces partial cross-correction of the disease by Yewande Pearse, Don Clarke, Shih-hsin Kan, Steven Q. Le, Valentina Sanghez, Anna Luzzi, Ivy Pham, Lina R. Nih, Jonathan D. Cooper, Patricia I. Dickson, Michelina Iacovino

    Get full text
    Article


  18. 18

    Neuropathology in mouse models of mucopolysaccharidosis type I, IIIA and IIIB. by Fiona L Wilkinson, Rebecca J Holley, Kia J Langford-Smith, Soumya Badrinath, Aiyin Liao, Alex Langford-Smith, Jonathan D Cooper, Simon A Jones, J Ed Wraith, Rob F Wynn, Catherine L R Merry, Brian W Bigger

    Published in PLoS ONE (2012-01-01)
    Get full text
    Article


  19. 19

    Neuronal deletion of the circadian clock gene Bmal1 induces cell-autonomous dopaminergic neurodegeneration by Michael F. Kanan, Patrick W. Sheehan, Jessica N. Haines, Pedro G. Gomez, Adya Dhuler, Collin J. Nadarajah, Zachary M. Wargel, Brittany M. Freeberg, Hemanth R. Nelvagal, Mariko Izumo, Joseph S. Takahashi, Jonathan D. Cooper, Albert A. Davis, Erik S. Musiek

    Published in JCI Insight (2024-07-01)
    Get full text
    Article


  20. 20

    Neuronal deletion of the circadian clock gene Bmal1 induces cell-autonomous dopaminergic neurodegeneration by Michael F. Kanan, Patrick W. Sheehan, Jessica N. Haines, Pedro G. Gomez, Adya Dhuler, Collin J. Nadarajah, Zachary M. Wargel, Brittany M. Freeberg, Hemanth R. Nelvagal, Mariko Izumo, Joseph S. Takahashi, Jonathan D. Cooper, Albert A. Davis, Erik S. Musiek

    Published in JCI Insight (2024-08-01)
    Get full text
    Article


Search Tools: