Search Results - Pierre Rustin

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  1. 1

    Correction: DAPIT Over-Expression Modulates Glucose Metabolism and Cell Behaviour in HEK293T Cells. by Heidi Kontro, Giuseppe Cannino, Pierre Rustin, Eric Dufour, Heikki Kainulainen

    Published in PLoS ONE (2015-01-01)
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  2. 2

    Correction: DAPIT Over-Expression Modulates Glucose Metabolism and Cell Behaviour in HEK293T Cells. by Heidi Kontro, Giuseppe Cannino, Pierre Rustin, Eric Dufour, Heikki Kainulainen

    Published in PLoS ONE (2015-01-01)
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  3. 3

    The variability of the harlequin mouse phenotype resembles that of human mitochondrial-complex I-deficiency syndromes. by Paule Bénit, Sergio Goncalves, Emmanuel Philippe Dassa, Jean-Jacques Brière, Pierre Rustin

    Published in PLoS ONE (2008-01-01)
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  4. 4

    Mouse studies to shape clinical trials for mitochondrial diseases: high fat diet in Harlequin mice. by Manuel Schiff, Paule Bénit, Riyad El-Khoury, Dimitri Schlemmer, Jean-François Benoist, Pierre Rustin

    Published in PLoS ONE (2011-01-01)
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  5. 5

    Succinate Dehydrogenase, Succinate, and Superoxides: A Genetic, Epigenetic, Metabolic, Environmental Explosive Crossroad by Paule Bénit, Judith Goncalves, Riyad El Khoury, Malgorzata Rak, Judith Favier, Anne-Paule Gimenez-Roqueplo, Pierre Rustin

    Published in Biomedicines (2022-07-01)
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  6. 6

    Paradoxical Inhibition of Glycolysis by Pioglitazone Opposes the Mitochondriopathy Caused by AIF Deficiency by Paule Bénit, Alice Pelhaître, Elise Saunier, Sylvie Bortoli, Assetou Coulibaly, Malgorzata Rak, Manuel Schiff, Guido Kroemer, Massimo Zeviani, Pierre Rustin

    Published in EBioMedicine (2017-03-01)
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  7. 7

    Mitochondrial temperature homeostasis resists external metabolic stresses by Mügen Terzioglu, Kristo Veeroja, Toni Montonen, Teemu O Ihalainen, Tiina S Salminen, Paule Bénit, Pierre Rustin, Young-Tae Chang, Takeharu Nagai, Howard T Jacobs

    Published in eLife (2023-12-01)
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  8. 8

    Mitochondria are physiologically maintained at close to 50 °C. by Dominique Chrétien, Paule Bénit, Hyung-Ho Ha, Susanne Keipert, Riyad El-Khoury, Young-Tae Chang, Martin Jastroch, Howard T Jacobs, Pierre Rustin, Malgorzata Rak

    Published in PLoS Biology (2018-01-01)
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  9. 9

    Translocator Protein-Mediated Stabilization of Mitochondrial Architecture during Inflammation Stress in Colonic Cells. by Leeyah Issop, Mariano A Ostuni, Sunghoon Lee, Mireille Laforge, Gabriel Péranzi, Pierre Rustin, Jean-François Benoist, Jérome Estaquier, Vassilios Papadopoulos, Jean-Jacques Lacapère

    Published in PLoS ONE (2016-01-01)
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  10. 10

    Pitfalls in Monitoring Mitochondrial Temperature Using Charged Thermosensitive Fluorophores by Dominique Chrétien, Paule Bénit, Christine Leroy, Riyad El-Khoury, Sunyou Park, Jung Yeol Lee, Young-Tae Chang, Guy Lenaers, Pierre Rustin, Malgorzata Rak

    Published in Chemosensors (2020-12-01)
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  11. 11

    Evolutionarily conserved susceptibility of the mitochondrial respiratory chain to SDHI pesticides and its consequence on the impact of SDHIs on human cultured cells. by Paule Bénit, Agathe Kahn, Dominique Chretien, Sylvie Bortoli, Laurence Huc, Manuel Schiff, Anne-Paule Gimenez-Roqueplo, Judith Favier, Pierre Gressens, Malgorzata Rak, Pierre Rustin

    Published in PLoS ONE (2019-01-01)
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  12. 12

    Alternative oxidase expression in the mouse enables bypassing cytochrome c oxidase blockade and limits mitochondrial ROS overproduction. by Riyad El-Khoury, Eric Dufour, Malgorzata Rak, Nelina Ramanantsoa, Nicolas Grandchamp, Zsolt Csaba, Bertrand Duvillié, Paule Bénit, Jorge Gallego, Pierre Gressens, Chamsy Sarkis, Howard T Jacobs, Pierre Rustin

    Published in PLoS Genetics (2013-01-01)
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  13. 13

    Author Correction: miR-379 links glucocorticoid treatment with mitochondrial response in Duchenne muscular dystrophy by Mathilde Sanson, Ai Vu Hong, Emmanuelle Massourides, Nathalie Bourg, Laurence Suel, Fatima Amor, Guillaume Corre, Paule Bénit, Inès Barthelemy, Stephane Blot, Anne Bigot, Christian Pinset, Pierre Rustin, Laurent Servais, Thomas Voit, Isabelle Richard, David Israeli

    Published in Scientific Reports (2024-03-01)
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  14. 14

    Sengers syndrome caused by biallelic TIMM29 variants and RNAi silencing in Drosophila orthologue recapitulates the human phenotype by Adel Shalata, Ann Saada, Mohammed Mahroum, Yarin Hadid, Chaya Furman, Zaher Eldin Shalata, Robert J. Desnick, Avraham Lorber, Asaad Khoury, Adnan Higazi, Avraham Shaag, Varda Barash, Ronen Spiegel, Euvgeni Vlodavsky, Pierre Rustin, Shmuel Pietrokovski, Irena Manov, Dan Gieger, Galit Tal, Adi Salzberg, Hanna Mandel

    Published in Human Genomics (2025-02-01)
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  15. 15

    Broad AOX expression in a genetically tractable mouse model does not disturb normal physiology by Marten Szibor, Praveen K. Dhandapani, Eric Dufour, Kira M. Holmström, Yuan Zhuang, Isabelle Salwig, Ilka Wittig, Juliana Heidler, Zemfira Gizatullina, Timur Gainutdinov, German Mouse Clinic Consortium, Helmut Fuchs, Valérie Gailus-Durner, Martin Hrabě de Angelis, Jatin Nandania, Vidya Velagapudi, Astrid Wietelmann, Pierre Rustin, Frank N. Gellerich, Howard T. Jacobs, Thomas Braun

    Published in Disease Models & Mechanisms (2017-02-01)
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  16. 16

    QIL1 mutation causes MICOS disassembly and early onset fatal mitochondrial encephalopathy with liver disease by Virginia Guarani, Claude Jardel, Dominique Chrétien, Anne Lombès, Paule Bénit, Clémence Labasse, Emmanuelle Lacène, Agnès Bourillon, Apolline Imbard, Jean-François Benoist, Imen Dorboz, Mylène Gilleron, Eric S Goetzman, Pauline Gaignard, Abdelhamid Slama, Monique Elmaleh-Bergès, Norma B Romero, Pierre Rustin, Hélène Ogier de Baulny, Joao A Paulo, J Wade Harper, Manuel Schiff

    Published in eLife (2016-09-01)
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