Terminal hemimyelocystocele associated with Chiari II malformation

Terminal myelocystocele (TMC) results from failure of embryonic CSF to drain outside the neural tube creating CSF reservoir within a dorsal meningocele. Association of Chiari II malformation with diastematomyelia and myelocystocele is extremely rare. Myelocystoceles do not have neural tissue so they...

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Bibliographic Details
Published in:Egyptian Pediatric Association Gazette
Main Authors: Umamaheswara Reddy V., Amit Agrawal, Kishor V. Hegde, Venugopal Sharma, Priya Malpani, Venkatesh Manchikanti
Format: Article
Language:English
Published: SpringerOpen 2014-06-01
Subjects:
Chiari malformation
Diastematomyelia
Myelocystocele
Spinal dysraphism
Online Access:http://www.sciencedirect.com/science/article/pii/S1110663814000287
Description
Summary:Terminal myelocystocele (TMC) results from failure of embryonic CSF to drain outside the neural tube creating CSF reservoir within a dorsal meningocele. Association of Chiari II malformation with diastematomyelia and myelocystocele is extremely rare. Myelocystoceles do not have neural tissue so they have good prognosis after treatment, however when associated with hydromelia and Chiari malformation they present with neurological deficits. We present details of a 2 year old female who presented to us with this rare anomaly.
ISSN:1110-6638

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