The prevalence of spontaneous pneumothorax in patients with BHD syndrome: a systematic review and meta-analysis

Abstract Background Birt-Hogg-Dubé (BHD) syndrome is associated with an increased risk of pneumothorax. This study aimed to determine the prevalence of spontaneous pneumothorax among individuals diagnosed with BHD syndrome. Method A comprehensive literature search was conducted across PubMed, EMBASE...

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Bibliographic Details
Published in:	Orphanet Journal of Rare Diseases
Main Authors:	Yanan Zhang, Yuling Wang, Jinxia Wang, Ping Li, Ruonan Lv, Juan Chen
Format:	Article
Language:	English
Published:	BMC 2025-05-01
Subjects:	Birt-Hogg-Dubé syndrome Spontaneous pneumothorax Folliculin Prevalence Meta-analysis
Online Access:	https://doi.org/10.1186/s13023-025-03726-z

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