Automated computed tomographic scoring of lung disease in adults with primary ciliary dyskinesia

Abstract Background The present study aimed to develop an automated computed tomography (CT) score based on the CT quantification of high-attenuating lung structures, in order to provide a quantitative assessment of lung structural abnormalities in patients with Primary Ciliary Dyskinesia (PCD). Met...

Full description

Bibliographic Details
Published in:	BMC Pulmonary Medicine
Main Authors:	Trieu-Nghi Hoang-Thi, Marie-Pierre Revel, Pierre-Régis Burgel, Laurence Bassinet, Isabelle Honoré, Thong Hua-Huy, Charlotte Martin, Bernard Maitre, Guillaume Chassagnon
Format:	Article
Language:	English
Published:	BMC 2018-12-01
Subjects:	Computed tomography Primary ciliary dyskinesia Kartagener syndrome Bronchiectasis
Online Access:	http://link.springer.com/article/10.1186/s12890-018-0758-6

Similar Items

Primary ciliary dyskinesia
by: Sandra Rovira-Amigo, et al.
Published: (2025-01-01)

Primary ciliary dyskinesia: A review
by: Shally Awasthi, et al.
Published: (2025-01-01)

EARLY DIAGNOSIS AND TREATMENT IN PATIENT WITH A PRIMARY CILIARY DYSKINESIA (KARTAGENER SYNDROME): CASE REPORT
by: I. V. Rybakova, et al.
Published: (2018-08-01)

Primary ciliary dyskinesia. Clinical observation
by: T. B. Pavlova, et al.
Published: (2016-02-01)

IJCM_83A: Primary Ciliary Dyskinesia in a child
by: Vasundhara J, et al.
Published: (2024-04-01)

A rare cause of acute abdominal pain in a patient with Primary ciliary dyskinesia with situs inversus totalis
by: Kısmet Çıkı, et al.
Published: (2020-02-01)

Primary ciliary dyskinesia as a rare cause of male infertility: case report and literature overview
by: Jan Novák, et al.
Published: (2024-12-01)

Why, when and how to investigate primary ciliary dyskinesia in adult patients with bronchiectasis
by: Martina Contarini, et al.
Published: (2018-08-01)

Primary Ciliary Dyskinesia: A Clinical Review
by: Katherine A. Despotes, et al.
Published: (2024-06-01)

Kartagener syndrome complicated by pulmonary tuberculosis, HIV, and hepatitis B: a rare case report
by: Thaodem Collin Singh, et al.
Published: (2025-07-01)

Kartagener’s Syndrome Presenting As Bilateral Recurrent Nasal Polyposis In A Young Boy
by: Zeba Ahmed, et al.
Published: (2018-10-01)

Kartagener syndrome in a young Ethiopian boy: a case report
by: Habtamu Mesele Gebray, et al.
Published: (2025-05-01)

Primary Ciliary Dyskinesia Complicated by Stroke in an Elderly Male: A Case Report
by: Ali Gohar, et al.
Published: (2025-03-01)

Kartagener's Syndrome With Complications: Diagnostic Challenges in a Resource‐Limited Setting
by: Nahid Afsar, et al.
Published: (2025-10-01)

Primary Ciliary Dyskinesia in Children
by: Alexander A. Baranov, et al.
Published: (2018-02-01)

Application of whole exome sequencing in patients with primary ciliary dyskinesia
by: Ke CHEN, et al.
Published: (2024-12-01)

Outcomes of Endoscopic Sinus Surgery for Chronic Rhinosinusitis in Adults with Primary Ciliary Dyskinesia
by: Diogo Barreto Plantier, et al.
Published: (2023-07-01)

Bilateral Hearing Loss in Primary Ciliary Dyskinesia: A Study of Conductive and Sensorineural Mechanisms from Pediatric and Adult Cases
by: Caroline Avgeri, et al.
Published: (2025-03-01)

Primary ciliary dyskinesia: Kartagener syndrome in a family with a novel DNAH5 gene mutation and variable phenotypes
by: Makia J. Marafie, et al.
Published: (2015-01-01)

Primary Ciliary Dyskinesia Registry
by: Mohammadreza Modaresi, et al.
Published: (2024-01-01)

Primary Ciliary Dyskinesia : A Case Presentation and A Current Review
by: Weerachai Tantinikorn, et al.
Published: (2020-08-01)

First report of DNAI2-associated primary ciliary dyskinesia in Libya: A case from a nonconsanguineous marriage
by: Ziyad Fathi Alatrash, et al.
Published: (2025-01-01)

Case Report: Primary ciliary dyskinesia due to CCNO mutations: a Chinese pediatric case series and literature review
by: Lejun Tong, et al.
Published: (2024-09-01)

Identification of Two Novel DNAAF2 Variants in Two Consanguineous Families with Primary Ciliary Dyskinesia
by: Lu C, et al.
Published: (2021-11-01)

Pneumonia and bacteremia due to Pseudomonas aeruginosa in a primary ciliary dyskinesia patient with DNAH5 variants: A case report
by: Ririko Shinozaki, et al.
Published: (2025-01-01)

Modern Approaches to the Diagnosis and Management of Children With Primary Ciliary Dyskinesia
by: A. A. Baranov, et al.
Published: (2017-05-01)

Clinical and Genetic Characterization of Patients with Primary Ciliary Dyskinesia in Southwest Saudi Arabia: A Cross Sectional Study
by: Ali Alsuheel Asseri, et al.
Published: (2023-10-01)

Primary ciliary dyskinesia
by: Plavec Goran, et al.
Published: (2004-01-01)

Ciliary Ultrastructure Assessed by Transmission Electron Microscopy in Adults with Bronchiectasis and Suspected Primary Ciliary Dyskinesia but Inconclusive Genotype
by: Ben O. Staar, et al.
Published: (2023-11-01)

Management of primary ciliary dyskinesia/Kartagener's syndrome in infertile male patients and current progress in defining the underlying genetic mechanism
by: Yan-Wei Sha, et al.
Published: (2014-02-01)

Primary ciliary dyskinesia: Meeting the challenges of diagnosis in South Africa
by: Z Dangor, et al.
Published: (2024-08-01)

Respiratory Distress in the Newborn with Primary Ciliary Dyskinesia
by: Evans Machogu, et al.
Published: (2021-02-01)

Kartagener Syndrome with Pan Atopic Airway Disease
by: Aakanksha, et al.
Published: (2022-09-01)

Kartagener′s syndrome
by: Pradip V Potdar, et al.
Published: (2012-01-01)

Kartagener′s syndrome in a fertile male - An uncommon variant
by: Barthwal M
Published: (2006-01-01)

National survey on pediatric respiratory physiotherapy units: primary ciliary dyskinesia and non-CF bronchiectasis
by: Beatrice Tani, et al.
Published: (2025-03-01)

The Swiss Primary Ciliary Dyskinesia registry: objectives, methods and first results
by: Myrofora Goutaki, et al.
Published: (2019-01-01)

Olfactory Dysfunction in Primary Ciliary Dyskinesia
by: Zainab Farzal, et al.
Published: (2025-01-01)

The Evaluation of Clinical and Genetic Characteristics of Primary Ciliary Dyskinesia
by: Melih Hangül, et al.
Published: (2022-08-01)

Bronchiectasis Assessment in Primary Ciliary Dyskinesia: A Non-Invasive Approach Using Forced Oscillation Technique
by: Wilfredo De Jesús-Rojas, et al.
Published: (2023-07-01)