What Is PFAPA and Why Does it Matter?
PFAPA, the syndrome of periodic fever, aphthous stomatitis, pharyngitis and cervical lymphadentitis, is an uncommon disease of episodic immune dysregulation that usually begins in early childhood. Symptoms occur at regular, predictable intervals, with healthy periods in between, and generally includ...
| Published in: | Journal of Patient-Centered Research and Reviews |
|---|---|
| Main Author: | Dennis J. Baumgardner |
| Format: | Article |
| Language: | English |
| Published: |
Advocate Aurora Health
2014-11-01
|
| Subjects: | |
| Online Access: | http://digitalrepository.aurorahealthcare.org/cgi/viewcontent.cgi?article=1036&context=jpcrr |
Similar Items
Case Report: PFAPA (Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Cervical Adenitis) Syndrome With a Novel TNFAIP3 Mutation
by: Jiewen Deng, et al.
Published: (2025-03-01)
by: Jiewen Deng, et al.
Published: (2025-03-01)
Challenges in the diagnosis of periodic fever, aphthous stomatitis, pharyngitis, and adenitis syndrome in developing countries—A decade of experience from North India
by: Aaqib Zaffar Banday, et al.
Published: (2022-09-01)
by: Aaqib Zaffar Banday, et al.
Published: (2022-09-01)
Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome
by: Ayşenur Paç Kısaarslan, et al.
Published: (2017-06-01)
by: Ayşenur Paç Kısaarslan, et al.
Published: (2017-06-01)
PFAPA (periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis) syndrome in children; surgical versus medical treatment?
by: Yuksel Toplu, et al.
Published: (2021-09-01)
by: Yuksel Toplu, et al.
Published: (2021-09-01)
Surgical management for periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis (PFAPA) syndrome: a systematic review and meta-analysis
by: Luís Fernando Ferreira Cavalcante, et al.
Published: (2025-07-01)
by: Luís Fernando Ferreira Cavalcante, et al.
Published: (2025-07-01)
Neglected adult PFAPA syndrome
by: Aiping Zhang, et al.
Published: (2025-04-01)
by: Aiping Zhang, et al.
Published: (2025-04-01)
Evaluation of common NLRP3 Q703K variant in pediatric patients with autoinflammatory disease: CAPS and PFAPA
by: Yasemin Kendir-Demirkol, et al.
Published: (2023-08-01)
by: Yasemin Kendir-Demirkol, et al.
Published: (2023-08-01)
Assessment of recurrent fever among children undergoing tonsillectomy
by: Mana Espahbodi, et al.
Published: (2024-12-01)
by: Mana Espahbodi, et al.
Published: (2024-12-01)
Paediatric PFAPA Syndrome: an Easily Missed Diagnosis
by: Nada Boutrid, et al.
Published: (2024-08-01)
by: Nada Boutrid, et al.
Published: (2024-08-01)
PFAPA (Periodic fever, aphtous stomatitis, pharingitis, cervical adenitis) or Marshall’s syndrome in children
by: N N Kuzmina, et al.
Published: (2005-10-01)
by: N N Kuzmina, et al.
Published: (2005-10-01)
A patient heterozygous for R92Q mutation with periodic fever and aphthous stomatitis, pharyngitis, and adenitis (PFAPA) syndrome-like phenotype
by: Ezgi Deniz Batu, et al.
Published: (2018-12-01)
by: Ezgi Deniz Batu, et al.
Published: (2018-12-01)
The effect of neutrophil-lymphocyte ratio and thrombocyte index on inflammation in patients with periodic fever, aphthous stomatitis, pharyngitis, and adenitis syndrome
by: Vildan Gungorer, et al.
Published: (2020-01-01)
by: Vildan Gungorer, et al.
Published: (2020-01-01)
Epidemiology and clinical features of PFAPA: a retrospective cohort study of 336 patients in western Sweden
by: Karin Rydenman, et al.
Published: (2022-09-01)
by: Karin Rydenman, et al.
Published: (2022-09-01)
Periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis syndrome persisting to adulthood – an example of a diagnostic and therapeutic challenge
by: Ewa Więsik-Szewczyk, et al.
Published: (2019-10-01)
by: Ewa Więsik-Szewczyk, et al.
Published: (2019-10-01)
COVID 19 vaccination as a trigger of acute genital ulcers in an immunocompromised adolescent—case study and literature review
by: Karolina Pokora, et al.
Published: (2024-03-01)
by: Karolina Pokora, et al.
Published: (2024-03-01)
PFAPA Syndrome: Evaluation of Clinical Findings, Immunological Alterations, and Treatment Approaches
by: Şefika İlknur Kökçü Karadağ, et al.
Published: (2024-08-01)
by: Şefika İlknur Kökçü Karadağ, et al.
Published: (2024-08-01)
Clinical features and diagnosis of PFAPA syndrome: approach of the primary care physician
by: Emiliia Burbela, et al.
Published: (2021-09-01)
by: Emiliia Burbela, et al.
Published: (2021-09-01)
Coexistence of PFAPA syndrome with separation anxiety
by: Yunus Emre Donmez, et al.
Published: (2019-03-01)
by: Yunus Emre Donmez, et al.
Published: (2019-03-01)
PFAPA-СИНДРОМ У ДІТЕЙ: ВИДАЛЯТИ ЧИ ЗБЕРІГАТИ МИГДАЛИКИ?
by: S. A. Levytska
Published: (2017-08-01)
by: S. A. Levytska
Published: (2017-08-01)
Response to cimetidine in a 1-year-old child with PFAPA syndrome
by: Kazuto Taniguchi, et al.
Published: (2016-12-01)
by: Kazuto Taniguchi, et al.
Published: (2016-12-01)
The use of ketotifen as long-term anti-inflammatory prophylaxis in children with PFAPA syndrome
by: Lenka Kapustova, et al.
Published: (2023-12-01)
by: Lenka Kapustova, et al.
Published: (2023-12-01)
Assessment of sleep in children with periodic fever, aphthous stomatitis, pharyngitis, and adenitis syndrome
by: Ayşin Nalbantoğlu, et al.
Published: (2021-08-01)
by: Ayşin Nalbantoğlu, et al.
Published: (2021-08-01)
Síndrome PFAPA - Caso clínico
by: Filipa Moreira, et al.
Published: (2012-06-01)
by: Filipa Moreira, et al.
Published: (2012-06-01)
Extreme Periodic Fever, Aphthous Stomatitis, Pharyngitis, Adenitis (PFAPA): a discrete group of patients
by: Mor Broide, et al.
Published: (2023-09-01)
by: Mor Broide, et al.
Published: (2023-09-01)
Diagnostic Criteria for Adult-Onset Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Cervical Adenitis (PFAPA) Syndrome
by: Luca Cantarini, et al.
Published: (2017-08-01)
by: Luca Cantarini, et al.
Published: (2017-08-01)
A Potential Link Between Outcome of Periodic Fever, Aphthous Stomatitis, Pharyngitis, Cervical Adenitis (PFAPA) Syndrome in Children and Breastfeeding: A Retrospective Single-Center Cohort Snapshot
by: Donato Rigante, et al.
Published: (2024-12-01)
by: Donato Rigante, et al.
Published: (2024-12-01)
Tonsillectomy in children with PFAPA-syndrome and Epstein-Barr viral infection
by: S. A. Levytska, et al.
Published: (2017-03-01)
by: S. A. Levytska, et al.
Published: (2017-03-01)
Рівень обізнаності лікарської спільноти із синдромом Маршалла (PFAPA)
by: E.I. Burbela, et al.
Published: (2024-10-01)
by: E.I. Burbela, et al.
Published: (2024-10-01)
Prevalence of Recurrent Aphthous Stomatitis in University Students and Its Relation with Anxiety
by: Atena Shiva, et al.
Published: (2019-12-01)
by: Atena Shiva, et al.
Published: (2019-12-01)
The therapeutic effect of systemic (oral) corticosteroids on the recurrent aphthous stomatitis: A systematic review
by: Elham Abbaszadeh, et al.
Published: (2022-01-01)
by: Elham Abbaszadeh, et al.
Published: (2022-01-01)
O Papel da Amigdalectomia na Síndrome de PFAPA: Revisão da Literatura e Estudo Retrospetivo
by: Pedro Gomes, et al.
Published: (2022-12-01)
by: Pedro Gomes, et al.
Published: (2022-12-01)
Olgu sunumu: PFAPA sendromu. “Periyodik yüksek ateş, aftöz stomatit, farenjit ve adenit”
by: Gaye Çelikcan, et al.
Published: (2012-03-01)
by: Gaye Çelikcan, et al.
Published: (2012-03-01)
Efficacy and safety of thalidomide for recurrent aphthous stomatitis: a systematic review and meta-analysis of randomized controlled trials
by: Yang Jian, et al.
Published: (2024-09-01)
by: Yang Jian, et al.
Published: (2024-09-01)
The Clinical Chameleon of Autoinflammatory Diseases in Children
by: Eugenio Sangiorgi, et al.
Published: (2022-07-01)
by: Eugenio Sangiorgi, et al.
Published: (2022-07-01)
Use of Streptococcus Salivarius K12 in a cohort of PFAPA patients
by: Alessandra Spagnolo, et al.
Published: (2024-07-01)
by: Alessandra Spagnolo, et al.
Published: (2024-07-01)
Colchicine versus cimetidine: the better choice for Periodic fever, aphthous stomatitis, pharyngitis, adenitis (PFAPA) syndrome prophylaxis, and the role of MEFV gene mutations
by: Seyed Reza Raeeskarami, et al.
Published: (2022-08-01)
by: Seyed Reza Raeeskarami, et al.
Published: (2022-08-01)
Quality of Life and Psychological Functioning in Children with PFAPA Syndrome
by: Xosé Ramón García-Soto, et al.
Published: (2025-04-01)
by: Xosé Ramón García-Soto, et al.
Published: (2025-04-01)
Periyodik ateş, aftöz stomatit, farenjit ve servikal adenit (PFAPA) sendromu: Bir olgu sunumu
by: Ruhuşen Kutlu, et al.
Published: (2018-03-01)
by: Ruhuşen Kutlu, et al.
Published: (2018-03-01)
Case Report: Identification of a CARD8 variant in all three patients with PFAPA syndrome complicated with Kawasaki disease
by: Haruhiko Nakamura, et al.
Published: (2024-03-01)
by: Haruhiko Nakamura, et al.
Published: (2024-03-01)
FIEBRE PERIÓDICA, AFTOSIS, FARINGITIS Y ADENITIS CERVICAL. NUESTRA EXPERIENCIA EN PACIENTES CON SÍNDROME PFAPA.
by: María Martín-Bailón, et al.
Published: (2016-02-01)
by: María Martín-Bailón, et al.
Published: (2016-02-01)
Similar Items
-
Case Report: PFAPA (Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Cervical Adenitis) Syndrome With a Novel TNFAIP3 Mutation
by: Jiewen Deng, et al.
Published: (2025-03-01) -
Challenges in the diagnosis of periodic fever, aphthous stomatitis, pharyngitis, and adenitis syndrome in developing countries—A decade of experience from North India
by: Aaqib Zaffar Banday, et al.
Published: (2022-09-01) -
Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome
by: Ayşenur Paç Kısaarslan, et al.
Published: (2017-06-01) -
PFAPA (periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis) syndrome in children; surgical versus medical treatment?
by: Yuksel Toplu, et al.
Published: (2021-09-01) -
Surgical management for periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis (PFAPA) syndrome: a systematic review and meta-analysis
by: Luís Fernando Ferreira Cavalcante, et al.
Published: (2025-07-01)
