Multiple congenital visceral abnormalities as a rare cause of pulmonary arterial hypertension

Abstract Background Pulmonary arterial hypertension (PAH) is a rare, progressive disorder. PAH is caused by a wide spectrum of pathologies but the cause remains undetermined on many occasions and patients are classified in the idiopathic group. Case presentation Here we report a young woman with rar...

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Bibliographic Details
Published in:The Egyptian Heart Journal
Main Authors: Parham Rabiee, Sedigheh Saedi
Format: Article
Language:English
Published: SpringerOpen 2022-04-01
Subjects:
Congenital heart disease
Pulmonary hypertension
Mayer–Rokitansky–Küster–Hauser syndrome
Abernethy malformation
Online Access:https://doi.org/10.1186/s43044-022-00273-x
Description
Summary:Abstract Background Pulmonary arterial hypertension (PAH) is a rare, progressive disorder. PAH is caused by a wide spectrum of pathologies but the cause remains undetermined on many occasions and patients are classified in the idiopathic group. Case presentation Here we report a young woman with rare congenital visceral abnormalities presenting with severe pulmonary hypertension. Conclusions Pulmonary hypertension is a complex disorder. Search for uncommon conditions that lead to pulmonary hypertension is necessary to determine the best management options.
ISSN:2090-911X

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