Multiple congenital visceral abnormalities as a rare cause of pulmonary arterial hypertension
Abstract Background Pulmonary arterial hypertension (PAH) is a rare, progressive disorder. PAH is caused by a wide spectrum of pathologies but the cause remains undetermined on many occasions and patients are classified in the idiopathic group. Case presentation Here we report a young woman with rar...
| 出版年: | The Egyptian Heart Journal |
|---|---|
| 主要な著者: | , |
| フォーマット: | 論文 |
| 言語: | 英語 |
| 出版事項: |
SpringerOpen
2022-04-01
|
| 主題: | |
| オンライン･アクセス: | https://doi.org/10.1186/s43044-022-00273-x |
| _version_ | 1851886774356279296 |
|---|---|
| author | Parham Rabiee Sedigheh Saedi |
| author_facet | Parham Rabiee Sedigheh Saedi |
| author_sort | Parham Rabiee |
| collection | DOAJ |
| container_title | The Egyptian Heart Journal |
| description | Abstract Background Pulmonary arterial hypertension (PAH) is a rare, progressive disorder. PAH is caused by a wide spectrum of pathologies but the cause remains undetermined on many occasions and patients are classified in the idiopathic group. Case presentation Here we report a young woman with rare congenital visceral abnormalities presenting with severe pulmonary hypertension. Conclusions Pulmonary hypertension is a complex disorder. Search for uncommon conditions that lead to pulmonary hypertension is necessary to determine the best management options. |
| format | Article |
| id | doaj-art-5a7bbb1d22bb4dcca7fc5ca63ef9db1d |
| institution | Directory of Open Access Journals |
| issn | 2090-911X |
| language | English |
| publishDate | 2022-04-01 |
| publisher | SpringerOpen |
| record_format | Article |
| spelling | doaj-art-5a7bbb1d22bb4dcca7fc5ca63ef9db1d2025-08-19T22:11:15ZengSpringerOpenThe Egyptian Heart Journal2090-911X2022-04-017411410.1186/s43044-022-00273-xMultiple congenital visceral abnormalities as a rare cause of pulmonary arterial hypertensionParham Rabiee0Sedigheh Saedi1Radiology Department, Rajaei Cardiovascular Medical and Research Center, Iran University of Medical SciencesCardiology and Adult Congenital Heart Disease Department, Rajaei Cardiovascular Medical and Research Center, Iran University of Medical SciencesAbstract Background Pulmonary arterial hypertension (PAH) is a rare, progressive disorder. PAH is caused by a wide spectrum of pathologies but the cause remains undetermined on many occasions and patients are classified in the idiopathic group. Case presentation Here we report a young woman with rare congenital visceral abnormalities presenting with severe pulmonary hypertension. Conclusions Pulmonary hypertension is a complex disorder. Search for uncommon conditions that lead to pulmonary hypertension is necessary to determine the best management options.https://doi.org/10.1186/s43044-022-00273-xCongenital heart diseasePulmonary hypertensionMayer–Rokitansky–Küster–Hauser syndromeAbernethy malformation |
| spellingShingle | Parham Rabiee Sedigheh Saedi Multiple congenital visceral abnormalities as a rare cause of pulmonary arterial hypertension Congenital heart disease Pulmonary hypertension Mayer–Rokitansky–Küster–Hauser syndrome Abernethy malformation |
| title | Multiple congenital visceral abnormalities as a rare cause of pulmonary arterial hypertension |
| title_full | Multiple congenital visceral abnormalities as a rare cause of pulmonary arterial hypertension |
| title_fullStr | Multiple congenital visceral abnormalities as a rare cause of pulmonary arterial hypertension |
| title_full_unstemmed | Multiple congenital visceral abnormalities as a rare cause of pulmonary arterial hypertension |
| title_short | Multiple congenital visceral abnormalities as a rare cause of pulmonary arterial hypertension |
| title_sort | multiple congenital visceral abnormalities as a rare cause of pulmonary arterial hypertension |
| topic | Congenital heart disease Pulmonary hypertension Mayer–Rokitansky–Küster–Hauser syndrome Abernethy malformation |
| url | https://doi.org/10.1186/s43044-022-00273-x |
| work_keys_str_mv | AT parhamrabiee multiplecongenitalvisceralabnormalitiesasararecauseofpulmonaryarterialhypertension AT sedighehsaedi multiplecongenitalvisceralabnormalitiesasararecauseofpulmonaryarterialhypertension |