A case of Kasabach-Merritt Syndrome in a nine-month-old; a rare complication of haemangioma in the young

Kasabach-Merritt Phenomenon (KMP) is a life-threatening consumptive coagulopathy that commonly occurs in infants and young children. It is a combination of an enlarging vascular lesion, thrombocytopenia, microangiopathic haemolytic anaemia, and hypofibrinogemia. The case of a nine-month-old child w...

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Bibliographic Details
Published in:Journal of the Pakistan Medical Association
Main Authors: Hafiz Khalid Pervaiz, Usman Jamil Mughal, Izza Ali Rai, Mumtaz Touseef, Aliezeh Fatima Rai
Format: Article
Language:English
Published: Pakistan Medical Association 2025-02-01
Subjects:
Haemangioma
Vincristine
Consumptive coagulopathy
KMP
Thrombocytopenia
Haemangioendothelioma
Online Access:https://jpma.org.pk/index.php/public_html/article/view/11607
Description
Summary:Kasabach-Merritt Phenomenon (KMP) is a life-threatening consumptive coagulopathy that commonly occurs in infants and young children. It is a combination of an enlarging vascular lesion, thrombocytopenia, microangiopathic haemolytic anaemia, and hypofibrinogemia. The case of a nine-month-old child who presented with a tuft haemangioma leading to the clinical features of KMP is presented. The investigation which was performed and pharmacological treatment initiated at different stages of presentation and the characteristic response to treatment are also discussed. Keywords: Haemangioma, Vincristine, Consumptive coagulopathy, KMP, Thrombocytopenia, Haemangioendothelioma.
ISSN:0030-9982

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