Microsurgical repair of a Terminal Myelocystocele: 2D operative video
An 8-month-old boy was referred to our department with a protruding soft mass in the lumbosacral region since birth, with intact overlying skin. The patient had clubfoot, and congenital scoliosis. On neurological examination, he had preserved muscle strength, but evolved with distal weakness and inc...
| الحاوية / القاعدة: | Archives of Pediatric Neurosurgery |
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| المؤلفون الرئيسيون: | , , , |
| التنسيق: | مقال |
| اللغة: | الإنجليزية |
| منشور في: |
Brazilian Society for Pediatric Neurosurgery
2022-05-01
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| الموضوعات: | |
| الوصول للمادة أونلاين: | https://www.archpedneurosurg.com.br/sbnped2019/article/view/139 |
| _version_ | 1850412142723858432 |
|---|---|
| author | Cleiton Formentin Leo Gordiano Matias Andrei Fernandes Joaquim Enrico Ghizoni |
| author_facet | Cleiton Formentin Leo Gordiano Matias Andrei Fernandes Joaquim Enrico Ghizoni |
| author_sort | Cleiton Formentin |
| collection | DOAJ |
| container_title | Archives of Pediatric Neurosurgery |
| description | An 8-month-old boy was referred to our department with a protruding soft mass in the lumbosacral region since birth, with intact overlying skin. The patient had clubfoot, and congenital scoliosis. On neurological examination, he had preserved muscle strength, but evolved with distal weakness and increasing in the lumbar mass volume. MRI confirmed the diagnosis of terminal myelocystocele by the typical finding of a trumpet-like flaring meningocele. Terminal myelocystocele classically presents as a large lumbosacral mass with skin cover, containing fat, cerebrospinal fluid, and neural tissue1,2. The spinal cord herniates through the dysraphic spine and terminates at a neural placode, whereas the central canal opens into a CSF-filled, ependyma-lined cavity3. We present a 2D operative video comprising microsurgical repair of the defect, resection of the nonfunctional caudal cyst wall, reconstruction of the proximal neural placode, and duroplasty. |
| format | Article |
| id | doaj-art-948bb40f15f045c0b07c2fe3e0c1d760 |
| institution | Directory of Open Access Journals |
| issn | 2675-3626 |
| language | English |
| publishDate | 2022-05-01 |
| publisher | Brazilian Society for Pediatric Neurosurgery |
| record_format | Article |
| spelling | doaj-art-948bb40f15f045c0b07c2fe3e0c1d7602025-08-19T22:46:21ZengBrazilian Society for Pediatric NeurosurgeryArchives of Pediatric Neurosurgery2675-36262022-05-0152e1392022e139202210.46900/apn.v4i3(September-December).139171Microsurgical repair of a Terminal Myelocystocele: 2D operative videoCleiton Formentin0https://orcid.org/0000-0002-1940-3569Leo Gordiano Matias1https://orcid.org/0000-0001-8974-4302Andrei Fernandes Joaquim2https://orcid.org/0000-0003-2645-0483Enrico Ghizoni3https://orcid.org/0000-0002-0850-7039Department of Neurology, University of Campinas (UNICAMP), Campinas, São Paulo, BrazilDivision of Neurosurgery, Department of Neurology, University of Campinas, Campinas, São Paulo, BrazilDivision of Neurosurgery, Department of Neurology, University of Campinas, Campinas, São Paulo, BrazilHead of the Neurosurgery Division - Department of Neurology, University of Campinas (UNICAMP), Campinas, São Paulo, BrazilAn 8-month-old boy was referred to our department with a protruding soft mass in the lumbosacral region since birth, with intact overlying skin. The patient had clubfoot, and congenital scoliosis. On neurological examination, he had preserved muscle strength, but evolved with distal weakness and increasing in the lumbar mass volume. MRI confirmed the diagnosis of terminal myelocystocele by the typical finding of a trumpet-like flaring meningocele. Terminal myelocystocele classically presents as a large lumbosacral mass with skin cover, containing fat, cerebrospinal fluid, and neural tissue1,2. The spinal cord herniates through the dysraphic spine and terminates at a neural placode, whereas the central canal opens into a CSF-filled, ependyma-lined cavity3. We present a 2D operative video comprising microsurgical repair of the defect, resection of the nonfunctional caudal cyst wall, reconstruction of the proximal neural placode, and duroplasty.https://www.archpedneurosurg.com.br/sbnped2019/article/view/139dysraphismmyelocystocelelumbosacral mass |
| spellingShingle | Cleiton Formentin Leo Gordiano Matias Andrei Fernandes Joaquim Enrico Ghizoni Microsurgical repair of a Terminal Myelocystocele: 2D operative video dysraphism myelocystocele lumbosacral mass |
| title | Microsurgical repair of a Terminal Myelocystocele: 2D operative video |
| title_full | Microsurgical repair of a Terminal Myelocystocele: 2D operative video |
| title_fullStr | Microsurgical repair of a Terminal Myelocystocele: 2D operative video |
| title_full_unstemmed | Microsurgical repair of a Terminal Myelocystocele: 2D operative video |
| title_short | Microsurgical repair of a Terminal Myelocystocele: 2D operative video |
| title_sort | microsurgical repair of a terminal myelocystocele 2d operative video |
| topic | dysraphism myelocystocele lumbosacral mass |
| url | https://www.archpedneurosurg.com.br/sbnped2019/article/view/139 |
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