PATIENT-CENTRED SCREENING FOR PRIMARY IMMUNODEFICIENCY, A MULTI-STAGE DIAGNOSTIC PROTOCOL DESIGNED FOR NONIMMUNOLOGISTS: 2011 UPDATE

Abstract. Members of the European Society for Immunodeficiencies (ESID) and other colleagues have updated themulti-stage expert-opinion-based diagnostic protocol for non-immunologists incorporating newly defined primary immunodeficiency diseases (PIDs). The protocol presented here aims to increase t...

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Published in:Медицинская иммунология
Main Authors: E. de Vries, A. A. Cardona, A. H. Abdul Latiff, R. Badolato, N. Brodszki, A. J. Cant, J. Carbone, J. T. Casper, A. Ciznar, A. V. Cochino, B. Derfalvi, G. J. Driessen, R. Elfeky, D. El-Ghoneimy, T. Espanol, A. Etzioni, E. Gambineri, K. Gilmour, L. I. Gonzalez-Granado, M. N. Guseva, M. H. Haverkamp, M. Helminen, M. Honig, M. G. Kanariou, M. Kirschfink, C. Klein, T. W. Kuijpers, N. Kutukculer, B. Martire, I. Meyts, T. Niehues, C. Pignata, S. M. Reda, E. D. Renner, N. Rezaei, M. Rizzi, M. A. Sampalo Lainz, R. B. Sargur, A. Sediva, M. G. Seidel, S. L. Seneviratne, P. Soler-Palacin, A. Tommasini, K. Warnatz
Format: Article
Language:Russian
Published: St. Petersburg branch of the Russian Association of Allergologists and Clinical Immunologists 2014-07-01
Subjects:
Online Access:https://www.mimmun.ru/mimmun/article/view/665
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author E. de Vries
A. A. Cardona
A. H. Abdul Latiff
R. Badolato
N. Brodszki
A. J. Cant
J. Carbone
J. T. Casper
A. Ciznar
A. V. Cochino
B. Derfalvi
G. J. Driessen
R. Elfeky
D. El-Ghoneimy
T. Espanol
A. Etzioni
E. Gambineri
K. Gilmour
L. I. Gonzalez-Granado
M. N. Guseva
M. H. Haverkamp
M. Helminen
M. Honig
M. G. Kanariou
M. Kirschfink
C. Klein
T. W. Kuijpers
N. Kutukculer
B. Martire
I. Meyts
T. Niehues
C. Pignata
S. M. Reda
E. D. Renner
N. Rezaei
M. Rizzi
M. A. Sampalo Lainz
R. B. Sargur
A. Sediva
M. G. Seidel
S. L. Seneviratne
P. Soler-Palacin
A. Tommasini
K. Warnatz
author_facet E. de Vries
A. A. Cardona
A. H. Abdul Latiff
R. Badolato
N. Brodszki
A. J. Cant
J. Carbone
J. T. Casper
A. Ciznar
A. V. Cochino
B. Derfalvi
G. J. Driessen
R. Elfeky
D. El-Ghoneimy
T. Espanol
A. Etzioni
E. Gambineri
K. Gilmour
L. I. Gonzalez-Granado
M. N. Guseva
M. H. Haverkamp
M. Helminen
M. Honig
M. G. Kanariou
M. Kirschfink
C. Klein
T. W. Kuijpers
N. Kutukculer
B. Martire
I. Meyts
T. Niehues
C. Pignata
S. M. Reda
E. D. Renner
N. Rezaei
M. Rizzi
M. A. Sampalo Lainz
R. B. Sargur
A. Sediva
M. G. Seidel
S. L. Seneviratne
P. Soler-Palacin
A. Tommasini
K. Warnatz
author_sort E. de Vries
collection DOAJ
container_title Медицинская иммунология
description Abstract. Members of the European Society for Immunodeficiencies (ESID) and other colleagues have updated themulti-stage expert-opinion-based diagnostic protocol for non-immunologists incorporating newly defined primary immunodeficiency diseases (PIDs). The protocol presented here aims to increase the awareness of PIDs among doctors working in different fields. Prompt identification of PID is important for prognosis, but this may not be an easy task. The protocol therefore starts from the clinical presentation of the patient. Because PIDs may present at all ages, this protocol is aimed at both adult and paediatric physicians. The multi-stage design allows cost-effective screening for PID of the large number of potential cases in the early phases, with more expensive tests reserved for definitive classification in collaboration with a specialist in the field of immunodeficiency at a later stage.
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spelling doaj-art-9cb9fdcb7bfa4429832701b902e8a2e12025-10-24T12:59:31ZrusSt. Petersburg branch of the Russian Association of Allergologists and Clinical ImmunologistsМедицинская иммунология1563-06252313-741X2014-07-0115547749210.15789/1563-0625-2013-5-477-492662PATIENT-CENTRED SCREENING FOR PRIMARY IMMUNODEFICIENCY, A MULTI-STAGE DIAGNOSTIC PROTOCOL DESIGNED FOR NONIMMUNOLOGISTS: 2011 UPDATEE. de Vries0A. A. Cardona1A. H. Abdul Latiff2R. Badolato3N. Brodszki4A. J. Cant5J. Carbone6J. T. Casper7A. Ciznar8A. V. Cochino9B. Derfalvi10G. J. Driessen11R. Elfeky12D. El-Ghoneimy13T. Espanol14A. Etzioni15E. Gambineri16K. Gilmour17L. I. Gonzalez-Granado18M. N. Guseva19M. H. Haverkamp20M. Helminen21M. Honig22M. G. Kanariou23M. Kirschfink24C. Klein25T. W. Kuijpers26N. Kutukculer27B. Martire28I. Meyts29T. Niehues30C. Pignata31S. M. Reda32E. D. Renner33N. Rezaei34M. Rizzi35M. A. Sampalo Lainz36R. B. Sargur37A. Sediva38M. G. Seidel39S. L. Seneviratne40P. Soler-Palacin41A. Tommasini42K. Warnatz43Jeroen Bosch Hospital ’s-HertogenboschInstituto Nacional de Pediatr a, Universidad Aut noma de M xico, Ciudad de MexicoDivision of Clinical Immunology and Paediatrics School of Medicine and Health Sciences, Monash University, Sunway CampusClinica Pediatrica dell’Universit di Brescia c/o Spedali Civili, Brescia, ItalyLund University Hospital, LundGreat North Children’s Hospital, Newcastle upon TyneDepartment of Immunology, Gregorio Mara on Hospital, MadridMedical College of Wisconsin, MACC Fund Research Center, MilwaukeeComenius University Medical School, Children’ University Hospital, BratislavaUniversity of Medicine and Pharmacy ‘Carol Davila’, BucharestSemmelweis University Budapest, BudapestErasmus MC, University Medical Center Rotterdam, RotterdamAin Shams University, CairoAin Shams University, CairoUniversity Hospital Vall d’Hebron, BarcelonaMeyer’s Children Hospital, Faculty of Medicine, Technion, HaifaUniversity of Florence, ‘Anna Meyer’ Children’s Hospital, FlorenceGreat Ormond Street for Children NHS Trust, LondonHospital 12 octubre, MadridSt. Petersburg Pediatric Medical Academy, St. PetersburgLeiden University Medical Center, LeidenUniversity Hospital of Tampere, TampereUniversity Hospital Ulm, UlmSpecific Center & Referral Center for Primary Immunodeficiencies – Paediatric Immunology, ‘Aghia Sophia’ Children’s Hospital, AthensInstitute of Immunology, University of Heidelberg, HeidelbergUniversity Children’s Hospital, Dr von Haunersches Kinderspital, MunichEmma Children’s Hospital, Academic Medical Center, AmsterdamEge University, IzmirPoliclinico Universit di Bari, BariUniversity Hospitals Leuven, LeuvenHelios Klinikum Krefeld; Krefeld Immunodeficiency Centre KIDZ, Krefeld‘Federico II’ University, NaplesAin Shams University, CairoUniversity Children’s Hospital, Ludwig Maximilians Universit t, MunchenChildren’s Medical Center, Tehran University of Medical Sciences, TehranUniversity Medical Center Freiburg, FreiburgPuerta del Mar Universitary Hospital, CadizNorthern General Hospital, SheffieldInstitute of Immunology, University Hospital Motol, PragueSt Anna Children’s Hospital, ViennaSt Mary’s Hospital and Imperial College, LondonVall d’Hebron University Hospital, BarcelonaInstitute for Maternal and Child Health, IRCCS Burlo Garofolo, TriesteUniversity Hospital of Freiburg, FreiburgAbstract. Members of the European Society for Immunodeficiencies (ESID) and other colleagues have updated themulti-stage expert-opinion-based diagnostic protocol for non-immunologists incorporating newly defined primary immunodeficiency diseases (PIDs). The protocol presented here aims to increase the awareness of PIDs among doctors working in different fields. Prompt identification of PID is important for prognosis, but this may not be an easy task. The protocol therefore starts from the clinical presentation of the patient. Because PIDs may present at all ages, this protocol is aimed at both adult and paediatric physicians. The multi-stage design allows cost-effective screening for PID of the large number of potential cases in the early phases, with more expensive tests reserved for definitive classification in collaboration with a specialist in the field of immunodeficiency at a later stage.https://www.mimmun.ru/mimmun/article/view/665diagnostic protocolimmunological evaluationprimary immunodeficiency
spellingShingle E. de Vries
A. A. Cardona
A. H. Abdul Latiff
R. Badolato
N. Brodszki
A. J. Cant
J. Carbone
J. T. Casper
A. Ciznar
A. V. Cochino
B. Derfalvi
G. J. Driessen
R. Elfeky
D. El-Ghoneimy
T. Espanol
A. Etzioni
E. Gambineri
K. Gilmour
L. I. Gonzalez-Granado
M. N. Guseva
M. H. Haverkamp
M. Helminen
M. Honig
M. G. Kanariou
M. Kirschfink
C. Klein
T. W. Kuijpers
N. Kutukculer
B. Martire
I. Meyts
T. Niehues
C. Pignata
S. M. Reda
E. D. Renner
N. Rezaei
M. Rizzi
M. A. Sampalo Lainz
R. B. Sargur
A. Sediva
M. G. Seidel
S. L. Seneviratne
P. Soler-Palacin
A. Tommasini
K. Warnatz
PATIENT-CENTRED SCREENING FOR PRIMARY IMMUNODEFICIENCY, A MULTI-STAGE DIAGNOSTIC PROTOCOL DESIGNED FOR NONIMMUNOLOGISTS: 2011 UPDATE
diagnostic protocol
immunological evaluation
primary immunodeficiency
title PATIENT-CENTRED SCREENING FOR PRIMARY IMMUNODEFICIENCY, A MULTI-STAGE DIAGNOSTIC PROTOCOL DESIGNED FOR NONIMMUNOLOGISTS: 2011 UPDATE
title_full PATIENT-CENTRED SCREENING FOR PRIMARY IMMUNODEFICIENCY, A MULTI-STAGE DIAGNOSTIC PROTOCOL DESIGNED FOR NONIMMUNOLOGISTS: 2011 UPDATE
title_fullStr PATIENT-CENTRED SCREENING FOR PRIMARY IMMUNODEFICIENCY, A MULTI-STAGE DIAGNOSTIC PROTOCOL DESIGNED FOR NONIMMUNOLOGISTS: 2011 UPDATE
title_full_unstemmed PATIENT-CENTRED SCREENING FOR PRIMARY IMMUNODEFICIENCY, A MULTI-STAGE DIAGNOSTIC PROTOCOL DESIGNED FOR NONIMMUNOLOGISTS: 2011 UPDATE
title_short PATIENT-CENTRED SCREENING FOR PRIMARY IMMUNODEFICIENCY, A MULTI-STAGE DIAGNOSTIC PROTOCOL DESIGNED FOR NONIMMUNOLOGISTS: 2011 UPDATE
title_sort patient centred screening for primary immunodeficiency a multi stage diagnostic protocol designed for nonimmunologists 2011 update
topic diagnostic protocol
immunological evaluation
primary immunodeficiency
url https://www.mimmun.ru/mimmun/article/view/665
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