Bilateral lung transplantation for pulmonary emphysema associated with cutis laxa

Cutis laxa is a rare elastic tissue disorder that mainly affects the skin and results in loss of elasticity. Occasionally, pulmonary emphysema complicates this condition. Herein, we report the first case of successful lung transplantation for severe juvenile emphysema associated with cutis laxa. The...

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Bibliographic Details
Published in:	JHLT Open
Main Authors:	Akira Matsumoto, Akihiro Ohsumi, Tomohiro Handa, Susumu Sato, Hiroyuki Katsuragawa, Hiroshi Date
Format:	Article
Language:	English
Published:	Elsevier 2024-05-01
Subjects:	cutis laxa lung transplantation elastic fiber disorder pulmonary emphysema lobar bronchial anastomosis
Online Access:	http://www.sciencedirect.com/science/article/pii/S2950133424000351

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