A rare immunological disease, caspase 8 deficiency: case report and literature review

Abstract Background Caspase-8 is a molecule in the FAS pathway that initiates apoptosis. One of the rarest autoimmune lymphoproliferative syndromes is caspase-8 deficiency. Immunodeficiency, splenomegaly, and lymphadenopathy are the common symptoms of this condition. Case Presentation A two-year-old...

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Bibliographic Details
Published in:	Allergy, Asthma & Clinical Immunology
Main Authors:	Narges Bazgir, Azin Tahvildari, Zahra Chavoshzade, Mahnaz Jamee, Zahra Golchehre, Abdollah Karimi, Naghi Dara, Mazdak Fallahi, Mohammad Keramatipour, Arezou Karamzade, Samin Sharafian
Format:	Article
Language:	English
Published:	BMC 2023-04-01
Online Access:	https://doi.org/10.1186/s13223-023-00778-3

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