Immunohistochemical alterations of dystrophin in congenital muscular dystrophy Alterações imuno-hístoquímicas da distrofina na distrofia muscular congênita

The dystrophin distribution in the plasma muscle membrane using immunohystochemistry was studied in 22 children with congenital muscular dystrophy. The dystrophin was detected by immunofluorescence in muscle biopsy through a polyclonal antibody. All the cases had patchy interruptions of the fluoresc...

وصف كامل

التفاصيل البيبلوغرافية
الحاوية / القاعدة:Arquivos de Neuro-Psiquiatria
المؤلفون الرئيسيون: Lineu Cesar Werneck, Eduardo Bonilla
التنسيق: مقال
اللغة:الإنجليزية
منشور في: Thieme Revinter Publicações 1995-09-01
الموضوعات:
الوصول للمادة أونلاين:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1995000300008