Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement

Rosai Dorfman disease is a rare but benign and self-limiting disorder. A case of Rosai Dorfman disease in a 16-year-old female with classic radiological and pathological findings is presented. T2W hypointense signal of the soft tissue masses was a distinguishing MRI feature. Contribution: Rosai Dor...

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Bibliographic Details
Published in:South African Journal of Radiology
Main Authors: Smily Sharma, Poonam Sherwani, Venkata S. Arunachalam, Rahul Dev
Format: Article
Language:English
Published: AOSIS 2023-10-01
Subjects:
rosai dorfman disease
emperipolesis
massive lymphadenopathy
sinus histiocytosis
histiocytosis.
Online Access:https://sajr.org.za/index.php/sajr/article/view/2729
Description
Summary:Rosai Dorfman disease is a rare but benign and self-limiting disorder. A case of Rosai Dorfman disease in a 16-year-old female with classic radiological and pathological findings is presented. T2W hypointense signal of the soft tissue masses was a distinguishing MRI feature. Contribution: Rosai Dorfman disease is often overlooked in the differentials of lymphadenopathy and soft tissue masses on account of its rarity. This case report comprehensively discusses the imaging approach to this rare disorder.
ISSN:1027-202X
2078-6778

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