Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement
Rosai Dorfman disease is a rare but benign and self-limiting disorder. A case of Rosai Dorfman disease in a 16-year-old female with classic radiological and pathological findings is presented. T2W hypointense signal of the soft tissue masses was a distinguishing MRI feature. Contribution: Rosai Dor...
| Published in: | South African Journal of Radiology |
|---|---|
| Main Authors: | , , , |
| Format: | Article |
| Language: | English |
| Published: |
AOSIS
2023-10-01
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| Subjects: | |
| Online Access: | https://sajr.org.za/index.php/sajr/article/view/2729 |
| _version_ | 1851884159873581056 |
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| author | Smily Sharma Poonam Sherwani Venkata S. Arunachalam Rahul Dev |
| author_facet | Smily Sharma Poonam Sherwani Venkata S. Arunachalam Rahul Dev |
| author_sort | Smily Sharma |
| collection | DOAJ |
| container_title | South African Journal of Radiology |
| description | Rosai Dorfman disease is a rare but benign and self-limiting disorder. A case of Rosai Dorfman disease in a 16-year-old female with classic radiological and pathological findings is presented. T2W hypointense signal of the soft tissue masses was a distinguishing MRI feature.
Contribution: Rosai Dorfman disease is often overlooked in the differentials of lymphadenopathy and soft tissue masses on account of its rarity. This case report comprehensively discusses the imaging approach to this rare disorder. |
| format | Article |
| id | doaj-art-e094cef30a6544fcb7f8ff3ec5b2ae28 |
| institution | Directory of Open Access Journals |
| issn | 1027-202X 2078-6778 |
| language | English |
| publishDate | 2023-10-01 |
| publisher | AOSIS |
| record_format | Article |
| spelling | doaj-art-e094cef30a6544fcb7f8ff3ec5b2ae282025-08-19T22:12:03ZengAOSISSouth African Journal of Radiology1027-202X2078-67782023-10-01271e1e610.4102/sajr.v27i1.27291237Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvementSmily Sharma0Poonam Sherwani1Venkata S. Arunachalam2Rahul Dev3Department of Diagnostic and Interventional Radiology, All India Institutes of Medical Sciences (AIIMS) Jodhpur, JodhpurDepartment of Radiodiagnosis, All India Institutes of Medical Sciences (AIIMS) Rishikesh, RishikeshDepartment of Imaging Sciences and Interventional Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, ThiruvananthapuramDepartment of Radiodiagnosis, All India Institutes of Medical Sciences (AIIMS) Rishikesh, RishikeshRosai Dorfman disease is a rare but benign and self-limiting disorder. A case of Rosai Dorfman disease in a 16-year-old female with classic radiological and pathological findings is presented. T2W hypointense signal of the soft tissue masses was a distinguishing MRI feature. Contribution: Rosai Dorfman disease is often overlooked in the differentials of lymphadenopathy and soft tissue masses on account of its rarity. This case report comprehensively discusses the imaging approach to this rare disorder.https://sajr.org.za/index.php/sajr/article/view/2729rosai dorfman diseaseemperipolesismassive lymphadenopathysinus histiocytosishistiocytosis. |
| spellingShingle | Smily Sharma Poonam Sherwani Venkata S. Arunachalam Rahul Dev Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement rosai dorfman disease emperipolesis massive lymphadenopathy sinus histiocytosis histiocytosis. |
| title | Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement |
| title_full | Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement |
| title_fullStr | Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement |
| title_full_unstemmed | Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement |
| title_short | Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement |
| title_sort | revisiting rosai dorfman disease a rare histiocytic disorder with nodal and extranodal involvement |
| topic | rosai dorfman disease emperipolesis massive lymphadenopathy sinus histiocytosis histiocytosis. |
| url | https://sajr.org.za/index.php/sajr/article/view/2729 |
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