Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement

Rosai Dorfman disease is a rare but benign and self-limiting disorder. A case of Rosai Dorfman disease in a 16-year-old female with classic radiological and pathological findings is presented. T2W hypointense signal of the soft tissue masses was a distinguishing MRI feature. Contribution: Rosai Dor...

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Published in:South African Journal of Radiology
Main Authors: Smily Sharma, Poonam Sherwani, Venkata S. Arunachalam, Rahul Dev
Format: Article
Language:English
Published: AOSIS 2023-10-01
Subjects:
Online Access:https://sajr.org.za/index.php/sajr/article/view/2729
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author Smily Sharma
Poonam Sherwani
Venkata S. Arunachalam
Rahul Dev
author_facet Smily Sharma
Poonam Sherwani
Venkata S. Arunachalam
Rahul Dev
author_sort Smily Sharma
collection DOAJ
container_title South African Journal of Radiology
description Rosai Dorfman disease is a rare but benign and self-limiting disorder. A case of Rosai Dorfman disease in a 16-year-old female with classic radiological and pathological findings is presented. T2W hypointense signal of the soft tissue masses was a distinguishing MRI feature. Contribution: Rosai Dorfman disease is often overlooked in the differentials of lymphadenopathy and soft tissue masses on account of its rarity. This case report comprehensively discusses the imaging approach to this rare disorder.
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2078-6778
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spelling doaj-art-e094cef30a6544fcb7f8ff3ec5b2ae282025-08-19T22:12:03ZengAOSISSouth African Journal of Radiology1027-202X2078-67782023-10-01271e1e610.4102/sajr.v27i1.27291237Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvementSmily Sharma0Poonam Sherwani1Venkata S. Arunachalam2Rahul Dev3Department of Diagnostic and Interventional Radiology, All India Institutes of Medical Sciences (AIIMS) Jodhpur, JodhpurDepartment of Radiodiagnosis, All India Institutes of Medical Sciences (AIIMS) Rishikesh, RishikeshDepartment of Imaging Sciences and Interventional Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, ThiruvananthapuramDepartment of Radiodiagnosis, All India Institutes of Medical Sciences (AIIMS) Rishikesh, RishikeshRosai Dorfman disease is a rare but benign and self-limiting disorder. A case of Rosai Dorfman disease in a 16-year-old female with classic radiological and pathological findings is presented. T2W hypointense signal of the soft tissue masses was a distinguishing MRI feature. Contribution: Rosai Dorfman disease is often overlooked in the differentials of lymphadenopathy and soft tissue masses on account of its rarity. This case report comprehensively discusses the imaging approach to this rare disorder.https://sajr.org.za/index.php/sajr/article/view/2729rosai dorfman diseaseemperipolesismassive lymphadenopathysinus histiocytosishistiocytosis.
spellingShingle Smily Sharma
Poonam Sherwani
Venkata S. Arunachalam
Rahul Dev
Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement
rosai dorfman disease
emperipolesis
massive lymphadenopathy
sinus histiocytosis
histiocytosis.
title Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement
title_full Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement
title_fullStr Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement
title_full_unstemmed Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement
title_short Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement
title_sort revisiting rosai dorfman disease a rare histiocytic disorder with nodal and extranodal involvement
topic rosai dorfman disease
emperipolesis
massive lymphadenopathy
sinus histiocytosis
histiocytosis.
url https://sajr.org.za/index.php/sajr/article/view/2729
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AT venkatasarunachalam revisitingrosaidorfmandiseaseararehistiocyticdisorderwithnodalandextranodalinvolvement
AT rahuldev revisitingrosaidorfmandiseaseararehistiocyticdisorderwithnodalandextranodalinvolvement