Ureteral switch for bilateral ureteropelvic junction obstruction in a case of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome
Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is characterized by congenital aplasia of the uterus and the upper part of the vagina. Secondary sexual characteristics and karyotype are normal. This syndrome affects at least 1 out of 4500 women. MRKH may be isolated (type I) but it is more frequently...
| Published in: | African Journal of Urology |
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| Main Authors: | , , , , |
| Format: | Article |
| Language: | English |
| Published: |
SpringerOpen
2013-12-01
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| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S1110570413000787 |
| _version_ | 1857081917697949696 |
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| author | L.E. Mubenga J. Lambertz A Feyaerts P Van Cangh F.X. Wese |
| author_facet | L.E. Mubenga J. Lambertz A Feyaerts P Van Cangh F.X. Wese |
| author_sort | L.E. Mubenga |
| collection | DOAJ |
| container_title | African Journal of Urology |
| description | Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is characterized by congenital aplasia of the uterus and the upper part of the vagina. Secondary sexual characteristics and karyotype are normal. This syndrome affects at least 1 out of 4500 women.
MRKH may be isolated (type I) but it is more frequently associated with other malformations (MRKH type II).
We present a typical case of MRKH type II associated with bilateral pelvic kidneys ectopia, ureteropelvic junction (UPJ) obstruction and high inserting ureters. The ureteral switch was performed at the time of pyeloplasty to prevent postoperative obstruction secondary to the angulation. |
| format | Article |
| id | doaj-art-e2afbf17f9af48a5b4b11f6c1227fffe |
| institution | Directory of Open Access Journals |
| issn | 1110-5704 |
| language | English |
| publishDate | 2013-12-01 |
| publisher | SpringerOpen |
| record_format | Article |
| spelling | doaj-art-e2afbf17f9af48a5b4b11f6c1227fffe2025-08-19T19:21:57ZengSpringerOpenAfrican Journal of Urology1110-57042013-12-0119418819010.1016/j.afju.2013.07.005Ureteral switch for bilateral ureteropelvic junction obstruction in a case of Mayer-Rokitansky-Küster-Hauser (MRKH) syndromeL.E. MubengaJ. LambertzA FeyaertsP Van CanghF.X. WeseMayer-Rokitansky-Küster-Hauser (MRKH) syndrome is characterized by congenital aplasia of the uterus and the upper part of the vagina. Secondary sexual characteristics and karyotype are normal. This syndrome affects at least 1 out of 4500 women. MRKH may be isolated (type I) but it is more frequently associated with other malformations (MRKH type II). We present a typical case of MRKH type II associated with bilateral pelvic kidneys ectopia, ureteropelvic junction (UPJ) obstruction and high inserting ureters. The ureteral switch was performed at the time of pyeloplasty to prevent postoperative obstruction secondary to the angulation.http://www.sciencedirect.com/science/article/pii/S1110570413000787Mayer-Rokitansky-Küster-Hauser syndromeUreteral switch |
| spellingShingle | L.E. Mubenga J. Lambertz A Feyaerts P Van Cangh F.X. Wese Ureteral switch for bilateral ureteropelvic junction obstruction in a case of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome Mayer-Rokitansky-Küster-Hauser syndrome Ureteral switch |
| title | Ureteral switch for bilateral ureteropelvic junction obstruction in a case of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome |
| title_full | Ureteral switch for bilateral ureteropelvic junction obstruction in a case of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome |
| title_fullStr | Ureteral switch for bilateral ureteropelvic junction obstruction in a case of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome |
| title_full_unstemmed | Ureteral switch for bilateral ureteropelvic junction obstruction in a case of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome |
| title_short | Ureteral switch for bilateral ureteropelvic junction obstruction in a case of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome |
| title_sort | ureteral switch for bilateral ureteropelvic junction obstruction in a case of mayer rokitansky kuster hauser mrkh syndrome |
| topic | Mayer-Rokitansky-Küster-Hauser syndrome Ureteral switch |
| url | http://www.sciencedirect.com/science/article/pii/S1110570413000787 |
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