Fatigability in spinal muscular atrophy: validity and reliability of endurance shuttle tests

Abstract Background To determine construct validity and test-retest reliability of Endurance Shuttle Tests as outcome measures for fatigability of remaining motor functions in children and adults with Spinal Muscular Atrophy (SMA) across the severity spectrum. Results We assessed the Endurance Shutt...

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Bibliographic Details
Published in:	Orphanet Journal of Rare Diseases
Main Authors:	Bart Bartels, Janke F. de Groot, Laura E. Habets, Camiel A. Wijngaarde, Wendy Vink, Marloes Stam, Fay-Lynn Asselman, Ruben P. A. van Eijk, W. Ludo van der Pol
Format:	Article
Language:	English
Published:	BMC 2020-03-01
Subjects:	Spinal muscular atrophy SMA Fatigability Endurance Outcome measure Muscle fatigue
Online Access:	http://link.springer.com/article/10.1186/s13023-020-1348-2

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