Dental and Anaesthetic Challenges in a Patient with Dystrophic Epidermolysis Bullosa

Epidermolysis bullosa is a group of rare genetic disorders characterised by skin and mucous membrane fragility and systemic manifestations of variable severity. We report a case of dystrophic epidermolysis bullosa in an 18-year-old male patient who presented to the Department of Oral Health at Sulta...

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Bibliographic Details
Published in:Sultan Qaboos University Medical Journal
Main Authors: Ali Al-Abadi, Salah A. Al-Azri, Abdulaziz Bakathir, Yusra Al-Riyami
Format: Article
Language:English
Published: Sultan Qaboos University 2016-11-01
Subjects:
dystrophic epidermolysis bullosa
dentistry
disease management
general anesthesia
case report
oman.
Online Access:https://journals.squ.edu.om/index.php/squmj/article/view/2192
Description
Summary:Epidermolysis bullosa is a group of rare genetic disorders characterised by skin and mucous membrane fragility and systemic manifestations of variable severity. We report a case of dystrophic epidermolysis bullosa in an 18-year-old male patient who presented to the Department of Oral Health at Sultan Qaboos University Hospital, Muscat, Oman, in 2015 with recurrent dental pain and infections. Due to the poor dental status of the patient and anticipated operative difficulties due to microstomia and limited mouth opening, the patient underwent full dental clearance under general anaesthesia. This article discusses the dental and anaesthetic challenges encountered during the management of this patient and provides a brief literature review.
ISSN:2075-051X
2075-0528

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