Search Results - Julien Ochala
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Aberrant myonuclear domains and impaired myofiber contractility despite marked hypertrophy in MYMK-related, Carey-Fineman-Ziter Syndrome by Hannah F. Dugdale, Yotam Levy, Heinz Jungbluth, Anders Oldfors, Julien Ochala
Published in Acta Neuropathologica Communications (2024-05-01)Get full text
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Sex-dependent and muscle-specific progression of the MYBPC1 E248K Myotrem myopathy in response to aging by Jennifer M. Mariano, Humberto C. Joca, Jacob Kallenbach, Natasha Ranu, Julien Ochala, Christopher Ward, Aikaterini Kontrogianni-Konstantopoulos
Published in JCI Insight (2025-08-01)Get full text
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Muscle fibre size and myonuclear positioning in trained and aged humans by Edmund Battey, Yotam Levy, Ross D. Pollock, Jamie N. Pugh, Graeme L. Close, Michaeljohn Kalakoutis, Norman R. Lazarus, Stephen D. R. Harridge, Julien Ochala, Matthew J. Stroud
Published in Experimental Physiology (2024-04-01)Get full text
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Ryanodine receptor type 1 content decrease‐induced endoplasmic reticulum stress is a hallmark of myopathies by Jeremy Vidal, Eric A. Fernandez, Martin Wohlwend, Pirkka‐Pekka Laurila, Andrea Lopez‐Mejia, Julien Ochala, Alexander J. Lobrinus, Bengt Kayser, Isabel C. Lopez‐Mejia, Nicolas Place, Nadège Zanou
Published in Journal of Cachexia, Sarcopenia and Muscle (2023-12-01)Get full text
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Increased cardiac myosin super-relaxation as an energy saving mechanism in hibernating grizzly bears by Robbert J. Van der Pijl, Weikang Ma, Christopher T.A. Lewis, Line Haar, Amalie Buhl, Gerrie P. Farman, Marcus Rhodehamel, Vivek P. Jani, O Lynne Nelson, Chengxin Zhang, Henk Granzier, Julien Ochala
Published in Molecular Metabolism (2025-02-01)Get full text
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A Laing distal myopathy–associated proline substitution in the β-myosin rod perturbs myosin cross-bridging activity by Massimo Buvoli, Genevieve C.K. Wilson, Ada Buvoli, Jack F. Gugel, Abbi Hau, Carsten G. Bönnemann, Carmen Paradas, David M. Ryba, Kathleen C. Woulfe, Lori A. Walker, Tommaso Buvoli, Julien Ochala, Leslie A. Leinwand
Published in The Journal of Clinical Investigation (2024-05-01)Get full text
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Impaired adaptive response to mechanical overloading in dystrophic skeletal muscle. by Pierre Joanne, Christophe Hourdé, Julien Ochala, Yvain Caudéran, Fadia Medja, Alban Vignaud, Etienne Mouisel, Wahiba Hadj-Said, Ludovic Arandel, Luis Garcia, Aurélie Goyenvalle, Rémi Mounier, Daria Zibroba, Kei Sakamoto, Gillian Butler-Browne, Onnik Agbulut, Arnaud Ferry
Published in PLoS ONE (2012-01-01)Get full text
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Activation of eIF4E‐binding‐protein‐1 rescues mTORC1‐induced sarcopenia by expanding lysosomal degradation capacity by Elisa M. Crombie, Seonyoung Kim, Stuart Adamson, Han Dong, Tzu‐Chiao Lu, Yiju Wu, Yajun Wu, Yotam Levy, Nolan Stimple, Wing Moon R. Lam, Hwee Weng D. Hey, Dominic J. Withers, Ao‐Lin Hsu, Boon Huat Bay, Julien Ochala, Shih‐Yin Tsai
Published in Journal of Cachexia, Sarcopenia and Muscle (2023-02-01)Get full text
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Human skeletal myopathy myosin mutations disrupt myosin head sequestration by Glenn Carrington, Abbi Hau, Sarah Kosta, Hannah F. Dugdale, Francesco Muntoni, Adele D’Amico, Peter Van den Bergh, Norma B. Romero, Edoardo Malfatti, Juan Jesus Vilchez, Anders Oldfors, Sander Pajusalu, Katrin Õunap, Marta Giralt-Pujol, Edmar Zanoteli, Kenneth S. Campbell, Hiroyuki Iwamoto, Michelle Peckham, Julien Ochala
Published in JCI Insight (2023-11-01)Get full text
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CaMKK2 is not involved in contraction-stimulated AMPK activation and glucose uptake in skeletal muscle by Florentina Negoita, Alex B. Addinsall, Kristina Hellberg, Conchita Fraguas Bringas, Paul S. Hafen, Tyler J. Sermersheim, Marianne Agerholm, Christopher T.A. Lewis, Danial Ahwazi, Naomi X.Y. Ling, Jeppe K. Larsen, Atul S. Deshmukh, Mohammad A. Hossain, Jonathan S. Oakhill, Julien Ochala, Jeffrey J. Brault, Uma Sankar, David H. Drewry, John W. Scott, Carol A. Witczak, Kei Sakamoto
Published in Molecular Metabolism (2023-09-01)Get full text
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Remodeling of skeletal muscle myosin metabolic states in hibernating mammals by Christopher TA Lewis, Elise G Melhedegaard, Marija M Ognjanovic, Mathilde S Olsen, Jenni Laitila, Robert AE Seaborne, Magnus Gronset, Changxin Zhang, Hiroyuki Iwamoto, Anthony L Hessel, Michel N Kuehn, Carla Merino, Nuria Amigo, Ole Frobert, Sylvain Giroud, James F Staples, Anna V Goropashnaya, Vadim B Fedorov, Brian Barnes, Oivind Toien, Kelly Drew, Ryan J Sprenger, Julien Ochala
Published in eLife (2024-05-01)Get full text
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Human skeletal muscle fiber heterogeneity beyond myosin heavy chains by Roger Moreno-Justicia, Thibaux Van der Stede, Ben Stocks, Jenni Laitila, Robert A. Seaborne, Alexia Van de Loock, Eline Lievens, Diana Samodova, Leyre Marín-Arraiza, Oksana Dmytriyeva, Robin Browaeys, Kim Van Vossel, Lukas Moesgaard, Nurten Yigit, Jasper Anckaert, Anneleen Weyns, Ruud Van Thienen, Ronni E. Sahl, Edmar Zanoteli, Michael W. Lawlor, Michael Wierer, Pieter Mestdagh, Jo Vandesompele, Julien Ochala, Morten Hostrup, Wim Derave, Atul S. Deshmukh
Published in Nature Communications (2025-02-01)Get full text
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