Case report: Successful use of sotatercept to treat pulmonary arterial hypertension in a patient with hereditary hemorrhagic telangiectasia

This case report describes a 45-year-old female with HHT type 1 (ENG mutation) and congenital heart disease (sinus venosus atrial septal defect and partial anomalous pulmonary venous return), diagnosed with severe PAH at age 16. Despite long-term treatment with epoprostenol, treprostinil, macitentan...

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Bibliographic Details

Published in:	Respiratory Medicine Case Reports
Main Authors:	Abinaya Ramakrishnan, Scott Olitsky, Rajan Saggar, Richard N. Channick, Justin P. McWilliams
Format:	Article
Language:	English
Published:	Elsevier 2025-01-01
Subjects:	Hereditary hemorrhagic telangiectasia Pulmonary arterial hypertension Sotatercept Epistaxis
Online Access:	http://www.sciencedirect.com/science/article/pii/S2213007125001571