Case report: Successful use of sotatercept to treat pulmonary arterial hypertension in a patient with hereditary hemorrhagic telangiectasia
This case report describes a 45-year-old female with HHT type 1 (ENG mutation) and congenital heart disease (sinus venosus atrial septal defect and partial anomalous pulmonary venous return), diagnosed with severe PAH at age 16. Despite long-term treatment with epoprostenol, treprostinil, macitentan...
| Published in: | Respiratory Medicine Case Reports |
|---|---|
| Main Authors: | Abinaya Ramakrishnan, Scott Olitsky, Rajan Saggar, Richard N. Channick, Justin P. McWilliams |
| Format: | Article |
| Language: | English |
| Published: |
Elsevier
2025-01-01
|
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2213007125001571 |
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