Deficiency of interleukin-1 receptor antagonist: An updated review of the pathogenesis, clinical characteristics, and treatments

Deficiency of Interleukin-1 receptor antagonist (DIRA) is a rare autosomal recessive autoinflammatory disease first reported in 2009. To date, 33 patients have been previously characterized and reported in literature. To the best of our knowledge, there have been no recent studies that have broadly...

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Bibliographic Details

Published in:	Clinical Immunology Communications
Main Authors:	Spencer Fang, Joshua Pillai, Baharullah Mahin
Format:	Article
Language:	English
Published:	Elsevier 2024-12-01
Subjects:	DIRA IL1RN IL-1Ra Autoinflammatory disease Deficiency of interleukin-1 receptor antagonist
Online Access:	http://www.sciencedirect.com/science/article/pii/S2772613424000131