Perioperative Management of Type-3c Gaucher's Disease for Kyphoscoliosis Correction and Spinal Cord Detethering

Gaucher's disease (GD) is an inherited lysosomal storage disorder caused by mutations in the acid β-glucosidase (GBA) gene, leading to abnormal function of the enzyme glucocerebrosidase, which results in the accumulation of glucocerebrosides in various organs, causing multiorgan dysfunction. GD...

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Bibliographic Details

Published in:	Journal of Neuroanaesthesiology and Critical Care
Main Authors:	Tasneem F. Ahmed, Ramamani Mariappan, Sreekumar M. Ramadas, Wilson P. D'Souza, Krishnaprabhu Raju
Format:	Article
Language:	English
Published:	Thieme Medical and Scientific Publishers Pvt. Ltd.
Subjects:	aortic stenosis type-3c Gaucher's disease kyphoscoliosis correction mitral stenosis massive blood loss and transfusion
Online Access:	http://www.thieme-connect.de/DOI/DOI?10.1055/s-0045-1811242