Autonomic dysfunction as the initial presentation in spinocerebellar ataxia type 3: A case report and review of the literature

Spinocerebellar ataxia type 3 (SCA3), as the most frequent autosomal dominant ataxia worldwide, is characterized by progressive cerebellar ataxia, dysarthria and extrapyramidal signs. Additionally, autonomic dysfunction, as a common clinical symptom, present in the later stage of SCA3. Here, we repo...

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Bibliographic Details
Published in:Frontiers in Neurology
Main Authors: Yi Jin, Yuchao Chen, Dan Li, Mengqiu Qiu, Menglu Zhou, Zhouyao Hu, Qiusi Cai, Xulin Weng, Xiaodong Lu, Bin Wu
Format: Article
Language:English
Published: Frontiers Media S.A. 2022-09-01
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Online Access:https://www.frontiersin.org/articles/10.3389/fneur.2022.967293/full