P075 | ERYTHROID STIMULATING AGENTS IN VEXAS SYNDROME: A MULTICENTER RETROSPECTIVE STUDY OF AN ITALIAN VEXAS COHORT

Background: VEXAS (Vacuoles, E1 Enzyme, X-linked, Autoinflammatory, Somatic) syndrome is an autoinflammatory disorder caused by UBA1 mutation. It manifests with inflammatory symptoms and commonly macrocytic anemia, which in up to 50% of cases meets WHO 2022 criteria for Myelodysplastic Neoplasia. Su...

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書誌詳細
出版年:Haematologica
主要な著者: G. Furnari, E. Diral, C. Campochiaro, F. Moretti, J. Ferrari, C. Elena, G. Battipaglia, S. Barbato, A. Vitale, M. Frigeni, F. Crisafulli, M. Frassi, C. Papayannidis, A. D. Romagnoli, C. Cattaneo, A. D’ambrosio, E. Morsia, P. Musto, G. Rivoli, M.E. Dragani, C. Toffalori, G.M. Bergonzi, G. Scorpio, A. Tomelleri, M.T. Voso, C. Gurnari, L. Vago, L. Dagna, F. Ciceri
フォーマット: 論文
言語:英語
出版事項: Ferrata Storti Foundation 2025-09-01
オンライン・アクセス:https://haematologica.org/article/view/12472