Pulmonary gas exchange in hereditary hemorrhagic telangiectasia patients with liver arteriovenous malformations

Abstract Background The severity of Hereditary Hemorrhagic Telangiectasia (HHT) disease is generally related to vascular visceral involvement represented by arteriovenous malformations (AVMs). Pulmonary function tests (PFTs) remain normal in HHT patients without Pulmonary AVMs (PAVMs) and respirator...

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Bibliographic Details

Published in:	Respiratory Research
Main Authors:	Carole de Picciotto, Mostafa El Hajjam, Carma Karam, Thierry Chinet, Marcel Bonay
Format:	Article
Language:	English
Published:	BMC 2019-07-01
Subjects:	Pulmonary diffusing capacity Arteriovenous malformations Hereditary hemorrhagic telangiectasia Computed tomography scan of the liver and chest Echocardiography
Online Access:	http://link.springer.com/article/10.1186/s12931-019-1106-y