Kartagener syndrome with pectus excavatum and upper lobar bronchiectasis

Primary Ciliary Dyskinesia (PCD) is a rare autosomal recessive disorder caused by impaired ciliary function. The incidence of PCD is 1 in 20,000 births. Kartagener's syndrome (KS), a subtype of PCD, is distinguished by the presence of situs inversus. KS occurs in about 1 in 32,000 to 40,000 bir...

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Bibliographic Details
Published in:Radiology Case Reports
Main Authors: Zain Saleem Khan, MD, Saransh Kumar Saini, MD, Weng Joe Chua, MD, Hao Ting (Jacky) Liao, MD, Samuel Manikkam, MD
Format: Article
Language:English
Published: Elsevier 2024-09-01
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Online Access:http://www.sciencedirect.com/science/article/pii/S1930043324005028