Segmental Absence of Intestinal Musculature in a Child with Type IV Ehlers–Danlos Syndrome

Patients with vascular Ehlers–Danlos syndrome (vEDS) have a defect in the formation of type III collagen. This defect puts patients at risk of vascular rupture, uterine rupture, and bowel perforations. The segmental absence of intestinal musculature is a rare histopathologic finding, wherein there i...

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Bibliographic Details

Published in:	Children
Main Authors:	Nicole Zeky, Celia Short, Brent Keith, Randall D. Craver, Jessica A. Zagory
Format:	Article
Language:	English
Published:	MDPI AG 2021-08-01
Subjects:	Ehlers–Danlos vascular Ehlers–Danlos intestinal perforation segmental absence of intestinal musculature
Online Access:	https://www.mdpi.com/2227-9067/8/8/680