Oxidative Stress in Cystinosis Patients

Oxidative Stress in Cystinosis Patients

Background/Aims: Nephropathic cystinosis (NC) is a severe systemic disease and cysteamine improves its prognosis. Lysosomal cystine accumulation is the hallmark of cystinosis and is regarded as the primary defect due to mutations in the CTNS gene. However, there is great evidence that cystine accumu...

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Bibliographic Details
Main Authors: Maria Helena Vaisbich, Luciana Pache de Faria Guimaraes, Maria Heloisa Mazzola Shimizu, Antonio Carlos Seguro
Format: Article
Language:English
Published: Karger Publishers 2011-09-01
Series:Nephron Extra
Subjects:
Biomarkers
Chronic kidney disease
Cysteamine
Cystinosis
End-stage renal disease
Oxidative stress
Thiobarbituric acid
Online Access:http://www.karger.com/Article/FullText/331445

Internet

http://www.karger.com/Article/FullText/331445

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