A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis

A 70-year-old female presented with a 4-week history of dry cough and wheezing. Chest radiograph showed a 10.5 cm mass-like density in the anterior mediastinum which had not been previously visualized. Computed tomography scan (CT) of the chest showed a right hilar mass encasing and narrowing right...

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Main Authors: Ghulam Rehman Mohyuddin, Fatima Sultan, Ghulam Khaleeq
Format: Article
Language:English
Published: Hindawi Limited 2012-01-01
Series:Case Reports in Pulmonology
Online Access:http://dx.doi.org/10.1155/2012/371490
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spelling doaj-0765e50826cb474880986afd251473662020-11-25T01:40:08ZengHindawi LimitedCase Reports in Pulmonology2090-68462090-68542012-01-01201210.1155/2012/371490371490A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid GranulomatosisGhulam Rehman Mohyuddin0Fatima Sultan1Ghulam Khaleeq2Department of Internal Medicine, Geisinger Medical Center, 100 North Academy Avenue, Danville, PA 17822, USADepartment of Internal Medicine, Geisinger Medical Center, 100 North Academy Avenue, Danville, PA 17822, USADivision of Pulmonary and Critical Care, Geisinger Medical Center, 100 North Academy Avenue, Danville, PA 17822, USAA 70-year-old female presented with a 4-week history of dry cough and wheezing. Chest radiograph showed a 10.5 cm mass-like density in the anterior mediastinum which had not been previously visualized. Computed tomography scan (CT) of the chest showed a right hilar mass encasing and narrowing right upper lobe bronchus and right mainstem bronchus and secondary atelectatic changes. Biopsy was consistent with a diagnosis of lymphomatoid granulomatosis Grade 3. She responded well clinically and radiologically to therapy. Lymphomatoid granulomatosis is a rare EBV-associated disorder which is considered a lymphoproliferative disease. The most common radiographic feature is multiple lung nodules. An isolated hilar mass is an exceptionally rare presentation of this rare disease.http://dx.doi.org/10.1155/2012/371490
collection DOAJ
language English
format Article
sources DOAJ
author Ghulam Rehman Mohyuddin
Fatima Sultan
Ghulam Khaleeq
spellingShingle Ghulam Rehman Mohyuddin
Fatima Sultan
Ghulam Khaleeq
A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis
Case Reports in Pulmonology
author_facet Ghulam Rehman Mohyuddin
Fatima Sultan
Ghulam Khaleeq
author_sort Ghulam Rehman Mohyuddin
title A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis
title_short A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis
title_full A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis
title_fullStr A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis
title_full_unstemmed A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis
title_sort rare presentation of a rare disease: pulmonary lymphomatoid granulomatosis
publisher Hindawi Limited
series Case Reports in Pulmonology
issn 2090-6846
2090-6854
publishDate 2012-01-01
description A 70-year-old female presented with a 4-week history of dry cough and wheezing. Chest radiograph showed a 10.5 cm mass-like density in the anterior mediastinum which had not been previously visualized. Computed tomography scan (CT) of the chest showed a right hilar mass encasing and narrowing right upper lobe bronchus and right mainstem bronchus and secondary atelectatic changes. Biopsy was consistent with a diagnosis of lymphomatoid granulomatosis Grade 3. She responded well clinically and radiologically to therapy. Lymphomatoid granulomatosis is a rare EBV-associated disorder which is considered a lymphoproliferative disease. The most common radiographic feature is multiple lung nodules. An isolated hilar mass is an exceptionally rare presentation of this rare disease.
url http://dx.doi.org/10.1155/2012/371490
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