Prune belly syndrome associated with bilateral multicystic dysplastic kidneys and urethral obstruction: A case report

Prune belly syndrome is a rare congenital disorder defined by a characteristic clinical triad: Abdominal muscle deficiency, severe urinary tract abnormalities, and bilateral cryptorchidism. We describe a preterm neonate of Prune Belly syndrome who had abdominal muscle deficiency, multicystic dysplas...

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Bibliographic Details
Main Authors: Arzu Akdag, Sule Arici, Betul Orhaner, Anil Dogan
Format: Article
Language:English
Published: Ped Urol Case Rep 2015-06-01
Series:Pediatric Urology Case Reports
Subjects:
Online Access:http://pediatricurologycasereports.com/ojs/index.php/pucr/article/view/79/53
Description
Summary:Prune belly syndrome is a rare congenital disorder defined by a characteristic clinical triad: Abdominal muscle deficiency, severe urinary tract abnormalities, and bilateral cryptorchidism. We describe a preterm neonate of Prune Belly syndrome who had abdominal muscle deficiency, multicystic dysplastic kidney, urethral hypoplasia and pulmonary hypoplasia. We presented this rare case with the data gathered from the literatüre.
ISSN:2148-2969
2148-2969